Bi-level positive airway pressure (BiPAP) ventilation in an infant with central hypoventilation syndrome

Villa, Maria Pia; Dotta, Andrea; Castello, D; Piro, Silvana; Pagani, Jacopo; Palamides, S; Ronchetti, R

doi:10.1002/(sici)1099-0496(199707)24:1<66::aid-ppul12>3.0.co;2-8

Cited by 53 publications

(11 citation statements)

References 11 publications

Supporting

Mentioning

Contrasting

Unclassified

Order By: Relevance

“…7 The youngest age at which nasal mask BiPAP has been applied for CCHS is 9 months. 8 However, no previous applications of nasal mask BiPAP for CCHS from the newborn period have been described.…”

Section: Discussionmentioning

confidence: 99%

“…9 Midface hypoplasia was recognized in a 7-year-old who had received nasal mask BiPAP since age 9 months for CCHS. 8 This was rectified by application of a Delaire mask (a standard orthodontic device) which allowed minimization of the pressure on the face. 10 Midface hypoplasia was reported in a 15-year-old after 10 years of nasal mask CPAP for obstructive sleep apnea.…”

Section: Discussionmentioning

confidence: 99%

See 1 more Smart Citation

Noninvasive ventilatory strategies in the management of a newborn infant and three children with congenital central hypoventilation syndrome

Tibballs

Henning

2003

Pediatric Pulmonology

View full text Add to dashboard Cite

Four children with congenital central hypoventilation syndrome (CCHS) treated with noninvasive techniques of ventilation are presented. Two infants (one in the newborn period) were treated with nasal mask bilevel positive airway pressure (BiPAP), and then both were transitioned to negative pressure chamber ventilation at several years of age because of possible midface hypoplasia. Tracheostomies were not performed. Two older children were transitioned from mechanical ventilation via tracheostomy to nasal mask BiPAP, and then in one case to negative pressure chamber ventilation, and in the other to phrenic nerve pacing. Their tracheostomies were removed.

show abstract

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Noninvasive ventilatory strategies in the management of a newborn infant and three children with congenital central hypoventilation syndrome

Tibballs

Henning

2003

Pediatric Pulmonology

View full text Add to dashboard Cite

show abstract

Section: Patient Coursementioning

confidence: 99%

“…To date, most children with CCHS are treated with positivepressure ventilation through permanent tracheotomy [16]. More recently, a few patients [10,16] have undergone a transition from invasive mechanical ventilation to a nasal mask. Gozal [7] has stated in a review of CCHS that such transitions generally fail in patients under 7 years old and in those who develop significant daytime alveolar hypoventilation.…”

Section: Patient Coursementioning

confidence: 99%

“…Gozal [7] has stated in a review of CCHS that such transitions generally fail in patients under 7 years old and in those who develop significant daytime alveolar hypoventilation. Villa et al [16] reported a 9-month old infant who successfully underwent noninvasive treatment. Our patient was able to have positivepressure ventilation via a nasal mask at 4 months of age, avoiding tracheotomy.…”

Section: Patient Coursementioning

confidence: 99%

See 1 more Smart Citation

Peculiar Respiratory Response Observed During Sleep-Onset REM Sleep of an Infant with Ondine's Curse

Takahashi

Kakizawa²,

Itou³

et al. 2000

Neuropediatrics

View full text Add to dashboard Cite

We treated an infant with congenital central hypoventilation syndrome ("Ondine's curse"). She was cyanotic and given ventilatory support at the first hour after birth. An investigation of sleep state and respiration performed at the age of 3 months led to this diagnosis. Hypoventilation persisted in all sleep stages, with the most severely reduced tidal volumes occurring during delta-wave sleep (stages 3 and 4). In addition, severe secondary reduction in tidal volumes occurred in sleep-onset REM sleep. This phenomenon was absent in non sleep-onset REM sleep. At 4 months of age, her respiratory treatment was successfully converted to positive-pressure ventilation via a nasal mask, thus avoiding tracheotomy. This transition to noninvasive ventilatory support dramatically improved her quality of life during wakefulness. This report may be a clue to discuss the function of sleep-onset REM sleep seen in the early stage of life and suggests that nasal mask ventilation is a viable option in selected cases with congenital central hypoventilation syndrome (CCHS).

show abstract

Congenital central hypoventilation syndrome: An update

Gozal

1998

Pediatr. Pulmonol.

155

View full text Add to dashboard Cite

Bi-level positive airway pressure (BiPAP) ventilation in an infant with central hypoventilation syndrome

Cited by 53 publications

References 11 publications

Noninvasive ventilatory strategies in the management of a newborn infant and three children with congenital central hypoventilation syndrome

Noninvasive ventilatory strategies in the management of a newborn infant and three children with congenital central hypoventilation syndrome

Peculiar Respiratory Response Observed During Sleep-Onset REM Sleep of an Infant with Ondine's Curse

Congenital central hypoventilation syndrome: An update

Contact Info

Product

Resources

About