Bilateral Chylothoraces As A Sentinel Presentation Of Primary AL Amyloidosis

Panchabhai, Tanmay S.; Kellie, Scott P.; Slone, Stephen P.; Cavallazzi, Rodrigo; Perez, Rafael L.; Yvette, M.

doi:10.1164/ajrccm-conference.2012.185.1_meetingabstracts.a5190

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“…It should be noted that pleural effusions might occur in AL amyloidosis as well as AA amyloidosis and Senile Systemic Amyloidosis [ 10 – 13 ]. Case reports have been published with pleural effusions present for each of these amyloidosis subtypes, and pleural fluid caused by AL amyloidosis has typically been documented to be composed of lymphocytic fluid with only two case reports of chylous fluid published in the current literature [ 14 ]. No clear association has been made for the pleural fluid composition and its occurrence, however.…”

Section: Discussionmentioning

confidence: 99%

Recurrent Pleural Effusions Occurring in Association with Primary Pulmonary Amyloidosis

Tada¹,

Anjum

Linville

et al. 2015

Case Reports in Pulmonology

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Recurrent pleural effusions occurring in association with immunoglobulin light chain amyloidosis and not associated with amyloid cardiomyopathy are rare. These portend an overall poor prognosis with mean survival time of approximately 1.8 months. We hereby report a case of a 59-year-old Caucasian female with recurrent pleural effusions and an ultimate diagnosis of pulmonary amyloidosis in association with plasma cell myeloma. The optimal treatment for recurrent pleural effusions in amyloidosis has not been determined; however, our patient responded to therapy with Cyclophosphamide-Bortezomib- (Velcade-) Dexamethasone (CyBorD) and had no repeat hospitalizations or recurrence of pleural effusion at four-month follow-up after initiation of therapy.

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Section: Discussionmentioning

confidence: 99%