Introduction: Internal jugular Phlebectasia is a rare finding seen with presentation of intermittent neck swelling increased in response to valsalva manoeuvre. It is usually presented early childhood, but it is diagnosed most frequently late due to its rarity. We present a case of right internal jugular phlebectasia followed by discussion regarding its presentation, diagnostic materials and management based on literature review.Case Report: A ten year old boy with no particular past medical history presented with a history of right neck intermittent swelling since birth, which became more prominent during the last 4years. Physical examination showed a non-pulsatile right side neck mass increasing in size by valsalva manoeuvre. Computed Tomography neck showed dilatation of right internal jugular vein which confirmed the diagnosis of Right Internal Jugular Phlebectasia.
Conclusion:Internal jugular phlebectasia is a rare condition, usually diagnosed late due to its rarity and lack of knowledge. It can be diagnosed clinically by demonstrating valsalva manoeuvre and looking for the neck swelling to occur. The best confirmatory investigation is Ultrasound combined with Colour Doppler Ultrasonography.