2018
DOI: 10.1212/nxi.0000000000000410
|View full text |Cite
|
Sign up to set email alerts
|

Brachio-cervical inflammatory myopathy with associated scleroderma phenotype and lupus serology

Help me understand this report

Search citation statements

Order By: Relevance

Paper Sections

Select...
3

Citation Types

2
12
0

Year Published

2020
2020
2024
2024

Publication Types

Select...
5
1

Relationship

0
6

Authors

Journals

citations
Cited by 6 publications
(14 citation statements)
references
References 7 publications
2
12
0
Order By: Relevance
“…Patients with BCIM usually associate other inflammatory diseases such as rheumatoid arthritis, lupus, or mixed connective tissue disease, but the association with SSc has been reported in few cases only. [1][2][3]12 Patients with SSc and myopathy have an important variability regarding clinical and histologic features. These patients may have just hyperCKemia or develop muscle weakness involving proximal muscles of the limbs.…”
Section: Discussionmentioning
confidence: 99%
See 1 more Smart Citation
“…Patients with BCIM usually associate other inflammatory diseases such as rheumatoid arthritis, lupus, or mixed connective tissue disease, but the association with SSc has been reported in few cases only. [1][2][3]12 Patients with SSc and myopathy have an important variability regarding clinical and histologic features. These patients may have just hyperCKemia or develop muscle weakness involving proximal muscles of the limbs.…”
Section: Discussionmentioning
confidence: 99%
“…1 There are less than 30 cases described in the literature so far. [1][2][3] In most of them, myositis was associated with other immune-mediated disorders such as myasthenia gravis, rheumatoid arthritis, or mixed connective tissue disease.…”
mentioning
confidence: 99%
“…After the first description of this entity, only few other reports have been published, mostly highlighting the prevalence of the disease among the female patients and the response to immunosuppressive agents. [8][9][10][11] MRI, that has been lately used in genetic and inflammatory myopathies for diagnostic purposes, sometimes providing specific patterns of involvement, and in follow-up, for the evaluation of disease progression and treatment response, has not been systematically investigated in BCIM. 12,13 Here, we report clinical and instrumental findings of patients followed at the Fondazione Policlinico Universitario A. Gemelli IRCCS affected by BCIM focusing on radiologic, histopathologic, and serologic assessments at baseline and after long-term follow-up.…”
Section: Discussionmentioning
confidence: 99%
“…A number of other additional therapies have been tried, including IVIg and plasma exchange or a combination of both, and the outcome was generally good in previously published BCIM cases. 7,[9][10][11] However, the heterogeneous treatment strategies make it difficult to select the best approach for a given patient, and the treatment choice is commonly guided by patients' comorbidities, side effects, and, finally, physicians' experience. In our population, this approach led to clinical and radiologic improvement in all but 1 patient.…”
Section: Discussionmentioning
confidence: 99%
“…Histopathological changes in muscle biopsy included variation in the sizes of the muscle fibers, necrosis, major histological compatibility (MHC)-I expression in muscle fibers, membrane attack complex (MAC) deposits, mononuclear (mainly CD20+ and CD4+ lymphocytes) and macrophage infil- Brachio-cervical inflammatory myopathy associated with systemic sclerosis ORIGINAL PAPER trates, and focal accumulations of mononuclear cells at the perimysium and perivascular sites (5). However, BCIM associated with SSc (BCIM-SSc) has been scarcely described in the literature (6)(7)(8)(9)(10)(11). Therefore, we aimed to report a series of four patients with BCIM-SSc from our tertiary center.…”
mentioning
confidence: 99%