Branch retinal artery occlusion with visual field and multifocal erg in Susac syndrome: a case report

Winden, Marianne van; Salu, P

doi:10.1007/s10633-010-9244-z

Cited by 11 publications

(9 citation statements)

References 18 publications

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“…These low VF and MP sensitivity signals observed in both eyes of this present case corresponded to the decreased perfusion seen on the OCTA density map. In spite of segmental VF defects had been reported in association with involved arterioles in SuS [ 17 – 19 ], the current case is the first to describe such association with OCTA.…”

Section: Discussionmentioning

confidence: 59%

Anatomical and functional correlation in Susac syndrome: multimodal imaging assessment

et al. 2017

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BackgroundSusac’s syndrome (SuS) is an uncommon disease characterized by retinal microangiopathy that may be assessed more accurately with optical coherence tomography angiography (OCTA), a new imaging technique which provides a retinal microvasculature map. The purpose of this case report is to describe the multimodal imaging findings of SuS correlating OCTA with functional tests.Case presentationRetrospective review of one case with clinical and imaging evidence of SuS. Color fundus photograph, fluorescein angiography (FA), OCTA, microperimetry (MP) and visual field (VF) tests were analyzed at the time of presentation and at 1- and 6-month visit following initiation of treatment. The study patient underwent standard treatment for SuS. The patient age was 31 year-old and the baseline visual acuity was 20/60 and 20/20 in the right and left eyes, respectively. At presentation, FA showed branch retinal arterial occlusion within the macular area of the right eye and vascular leakage in the periphery of the left eye. OCTA demonstrated areas of superficial and deep retinal vascular plexuses hypoperfusion in both eyes. The OCTA segmentations in the outer retina and choriocapillaris were normal. The low VF and MP sensitivity signals precisely corresponded to the topography of decreased vascular perfusion seen on the OCTA density map in both eyes. Six months after specific SuS therapy, retinal vascular perfusion showed partial improvement in both eyes.ConclusionOCTA may demonstrate superficial and deep retinal vascular non-perfusion without choriocapillary vasculature changes in SuS. This anatomical information given by OCTA corresponded to points of low sensitivity on functional tests represented by VF and MP.

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Section: Discussionmentioning

confidence: 59%

Anatomical and functional correlation in Susac syndrome: multimodal imaging assessment

et al. 2017

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“…[4] SS-associated retinal artery occlusions (multiple BRAOs) are important because similar to our patient they may cause severe visual loss. BRAO also can cause photopsia, black spots, and scintillating scotomas.…”

Section: Discussionmentioning

confidence: 61%

“…SS usually presents with a severe headache, transient personality and mental changes, progressive cognitive decline, and later by hearing loss, tinnitus, and segmental visual loss. [4] The first presentation of SS in our patient was severe loss of vision. Unlike our case, in SS, urinary incontinence and generalized seizure may happen, and the low-to-medium frequency sensory neural hearing loss may be permanent.…”

Section: Discussionmentioning

confidence: 88%

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Progressive Susac syndrome with bilateral visual loss and disability

Entezari

Karimi

Feizi

2016

Indian J Ophthalmol

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Susac syndrome (SS) is a rare retinal-cochlear-cerebral disease with an unclear etiology. A 35-year-old man presented with sudden painless vision loss in the right eye and 2 months later in the left eye with hemiparesis, behavioral changes, and hearing loss. Ophthalmic examinations revealed multiple branch retinal artery occlusions (BRAOs) in both eyes. Brain magnetic resonance imaging showed inflammatory changes with multiple “punched-out” lesions in the corpus callosum which confirmed the diagnosis of SS. Despite intravenous and oral corticosteroid therapy, the disease progressed with the development of new BRAOs, low vision in both eyes, and disability. Prompt diagnosis and early treatment may save the vision and even patient's life.

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“…Therefore, Susac syndrome should be kept in mind especially for young patients who have unexplained retinal artery occlusion in one eye. Aggressive steroid treatment in these patients may survive their healthy eye (5) .…”

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confidence: 99%

Progression of retinal artery occlusion from one eye to the other seems to be a characteristic finding in Susac syndrome

Yıldırım¹,

Kar²,

Kaya³

2013

Arq. Bras. Oftalmol.

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Branch retinal artery occlusion with visual field and multifocal erg in Susac syndrome: a case report

Cited by 11 publications

References 18 publications

Anatomical and functional correlation in Susac syndrome: multimodal imaging assessment

Anatomical and functional correlation in Susac syndrome: multimodal imaging assessment

Progressive Susac syndrome with bilateral visual loss and disability

Progression of retinal artery occlusion from one eye to the other seems to be a characteristic finding in Susac syndrome

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