Calcifying nested stromal-epithelial tumor of the liver with recurrence in a transplanted liver – A clinical report with literature review

Kamal, Maria; Atwi, Doaa; Gatalica, Zoran; Luo, Wei

doi:10.1016/j.hpr.2022.300620

Cited by 1 publication

(5 citation statements)

References 23 publications

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“…Chemotherapy (hepatoblastoma or soft-tissue sarcoma protocol-based) has also been reported in the literature. 2,9 Most of the reported cases had low-grade histology and followed an indolent clinical course. To the best of our knowledge, among the 50 reported cases, only 8 had a recurrence and 5 cases showed distant metastasis.…”

Section: Discussionmentioning

confidence: 99%

“…Chemotherapy (hepatoblastoma or soft-tissue sarcoma protocol-based) has also been reported in the literature. 2 , 9 …”

Section: Discussionmentioning

confidence: 99%

“…1 The histogenesis of this tumor remains unknown, but histologically, it has been described as a nonbiliary, nonhepatocytic tumor of the liver composed of nests of spindle and epithelioid cells along with a desmoplastic myofibroblastic stroma containing variable calcification and sometimes ossification as well. 2 Clinically, it may present with abdominal pain, a mass, ileus, or as an incidental finding in an asymptomatic patient. Various associations of CNSETs have been described in the literature, such as cortisol-related syndrome and Beckwith-Wiedemann syndrome.…”

Section: Introductionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

“…The tumor is more common among young children and female patients. 2 – 4 In this report, we present a patient who underwent right hepatectomy for a large CNSET.…”

Section: Introductionmentioning

confidence: 99%

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Calcifying Nested Stromal-Epithelial Tumor: An Extremely Rare Hepatic Tumor

Khan,

Syed,

Ulhaq

et al. 2023

ACG Case Rep J

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Calcifying nested stromal-epithelial tumor is a rare hepatic malignancy with approximately 50 cases reported in the literature. Its clinical presentation is nonspecific, and the diagnosis is mainly based on histology which shows nests of spindle and epithelioid cells along with a desmoplastic myofibroblastic stroma containing variable calcification and ossification. In this report, we present a case of a 24-year-old woman with a history of abdominal pain, distension, and dyspepsia. She had a palpable liver with normal liver function test results. Serum alpha-fetoprotein levels were within normal range, and serologies for hepatitis B and C virus remained negative. Radiological investigations (magnetic resonance imaging and computed tomography) showed a large, right hepatic lobe mass with tumor invasion into the right posterior portal vein, but the 2 modalities could not characterize the lesion. Finally, an ultrasound-guided biopsy of the liver lesion provided the diagnosis of calcifying nested stromal-epithelial tumor. The tumor was resected successfully.

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Section: Discussionmentioning

confidence: 99%

“…Chemotherapy (hepatoblastoma or soft-tissue sarcoma protocol-based) has also been reported in the literature. 2 , 9 …”

Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

“…The tumor is more common among young children and female patients. 2 – 4 In this report, we present a patient who underwent right hepatectomy for a large CNSET.…”

Section: Introductionmentioning

confidence: 99%

See 3 more Smart Citations