Calcinosis of the arteries with coronary calcification in infancy

Idiopathic arterial calcification in infancy

“…Including our case, three sick children demonstrating the I.A.C. syndrome were examinated by these techniques [1,8]. The X-ray demonstrated a stenosis or a complete occlusion of the trunks or the branches of the coronary arteries.…”

“…In the majority of cases, signs of heart failure are predominant [1,5,7]. They appear rapidly in the weeks following delivery.…”

“…is not the primary diagnosis. Only when calcifications of the systemic arteries can be demonstrated radiologically does the diagnosis become obvious [1].…”

“…The X-ray demonstrated a stenosis or a complete occlusion of the trunks or the branches of the coronary arteries. According to Beuren et al [1] it is advisable to collect more information before deciding on the specifity of the images, due to the few cases described in the literature.…”

“…Since the review of the literature made in 1966 by Gabilan et al [3] approximately a dozen cases have been published. The majority of the children died before six months of age and very few have lived more than one year [1,5]. With one exception [1] the diagnosis was only made after the pathologic examination of post mortem specimens and calcifications were found in the internal elastic lamina of the coronary arteries and the other muscular arteries.…”