“…Interestingly, all reported malignancies were located within the hepatobiliary system. For instance, one case detailed successful pancreatectomy for cancer of the terminal part of the common bile duct in a patient with disorientation of the pancreaticoduodenal complex [ 8 ]. Another case involved a young adult male in his twenties with left atrial isomerism and dextrocardia who developed multifocal metastatic hepatocellular carcinoma [ 9 ].…”