Cardiac Rhabdomyoma in the Neonate: Surgical Management

Foster, Eric D.; Spooner, Eric W.; Farina, Matthew A.; Shaher, Reda M.; Alley, Ralph D.

doi:10.1016/s0003-4975(10)60334-7

Cited by 45 publications

(14 citation statements)

References 11 publications

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“…2,3 However, echocardiography studies of cardiac rhabdomyoma have shown that this tumor is less ominous than was previously thought. 4,5 Cardiac rhabdomyoma in asymptomatic patients and in patients with tuberous sclerosis (TS) has been described. 4,5 Spontaneous regression of this tumor has also been documented.…”

mentioning

confidence: 99%

“…4,5 Cardiac rhabdomyoma in asymptomatic patients and in patients with tuberous sclerosis (TS) has been described. 4,5 Spontaneous regression of this tumor has also been documented. 4,5 The purpose of this study was to demonstrate the clinical presentation, echocardiographic findings, and morbidity and mortality rates for rhabdomyomas in Chinese infants and children.…”

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confidence: 99%

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Echocardiographic evaluation of cardiac rhabdomyoma in infants and children

Liang

Ko²,

Huang

2000

J. Clin. Ultrasound

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confidence: 99%

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confidence: 99%

Echocardiographic evaluation of cardiac rhabdomyoma in infants and children

Liang

Ko²,

Huang

2000

J. Clin. Ultrasound

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“…[12][13][14][15] Non-operated patients may have minimal cardiac signs or symptoms for several year, 15 whereas those with obstructive symptoms should be operated on as a matter of urgency. 16,17 Anatomic and hemodynamic abnormalities can be quickly determined by 2-D echocardiography. 18 In the present study, there was little discrepancy between echocardiography and EBT examination in tumor location.…”

Section: Discussionmentioning

confidence: 99%

Evaluation of Cardiac Tumors in Children by Electron-Beam Computed Tomography Rhabdomyoma and Fibroma

Sugiyama

Naito

Tsukano

et al. 2005

Circ J

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BackgroundThe most common cardiac tumors in young children are rhabdomyoma and fibroma, and prognosis depends on the tumor's characteristics. In the present study electron-beam computed tomography (EBT) was used to evaluate tumor characteristics and myocardial perfusion in 6 children with cardiac tumors. Methods and ResultsFive children had rhabdomyomas and 1 had a fibroma. In the precontrast study, the computed tomography numbers of rhabdomyomas were higher and those of the fibroma were slightly lower than those of the normal myocardium. In the early postcontrast study, the size, location, shape and number of the tumor were clearly detected, and in the late postcontrast study, the fibrous characteristics of the tumor were seen. The fibroma contained calcification and 2 rhabdomyomas contained a fat density spot. In the cine-mode study, both the tumor and ventricular wall motion could be simultaneously evaluated. There was a filling defect of the left ventricular myocardium on the early postcontrast scan of 1 child with a rhabdomyoma and dyskinetic wall motion at the same region in the cine-mode study. Conclusion EBT was useful for evaluating tumor characteristics in children. (Circ J 2005; 69: 1352 -1356

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“…Of patients with rhabdomyomas 30-50% will eventually manifest tuberous sclerosis (3). Since spontaneous regression of this tumor has been well documented, surgery is indicated only for palliative partial resection to relieve life-threatening outflow obstruction or lung compression (4,5).…”

Section: Discussionmentioning

confidence: 99%

Differentiation of Tumor from Viable Myocardium using Cardiac Tagging with MR Imaging

Bouton¹,

Yang²,

McCrindle³

et al. 1991

Journal of Computer Assisted Tomography

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We report the application of myocardial tagging by MR to define tissue planes and differentiate contractile from noncontractile tissue in a neonate with congenital cardiac rhabdomyoma. Using custom-written pulse programming software, six 2 mm thick radiofrequency (RF) slice-selective presaturation pulses (tags) were used to label the chest wall and myocardium in a star pattern in diastole, ∼60 ms before the R-wave gating trigger. This method successfully delineated the myocardium from noncontractile tumor, providing information that influenced clinical management. This RF tagging technique allowed us to confirm the exact intramyocardial location of a congenital cardiac tumor. KeywordsMagnetic resonance imaging; techniques-Heart; neoplasms-Heart; ventriclesIn the evaluation of neonatal thoracic tumors, precise localization of the tumor and differentiation from viable myocardium are critical in planning surgical treatment. We previously reported the use of myocardial tagging (1) using slice-selective radio-frequency (RF) presaturation followed by MR imaging in the orthogonal plane to evaluate regional leftventricular (LV) function. In this article we report the application of myocardial tagging by MR to define tissue planes and to differentiate contractile from noncontractile tissue in a patient with presumed congenital cardiac rhabdomyoma. CASE REPORTA 3-day-old infant was referred for MR evaluation of a thoracic mass detected first on fetal ultrasound and confirmed later by postnatal echocardiography. Following an uncomplicated vaginal delivery, the patient demonstrated persistent mild respiratory distress with tachypnea, tachycardia, hypoxemia, and hypercapnia. Physical examination showed a well-developed newborn girl with no evident external anomalies. Subcostal retractions and nasal flaring were noted and, on auscultation, a systolic ejection murmur was heard. There was no evidence of congestive heart failure.Chest roentgenography showed a very large cardiac silhouette with compression of the left lung (Fig. 1). Electrocardiography (ECG) showed greatly increased LV forces with marked

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Cardiac Rhabdomyoma in the Neonate: Surgical Management

Cited by 45 publications

References 11 publications

Echocardiographic evaluation of cardiac rhabdomyoma in infants and children

Echocardiographic evaluation of cardiac rhabdomyoma in infants and children

Evaluation of Cardiac Tumors in Children by Electron-Beam Computed Tomography Rhabdomyoma and Fibroma

Differentiation of Tumor from Viable Myocardium using Cardiac Tagging with MR Imaging

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