Cases of Atypical Lymphangiomas in Children

Abstract

Background. Lymphatic malformations or lymphangiomas are rare benign hamartomas that result from maldevelopment of primitive lymphatic sacs. They are most frequently found in the neck and axilla, while intra-abdominal and mediastinal lymphangiomas are uncommon. These are primarily tumours of infancy and childhood and are successfully treated with surgical excision. Summary of Cases. Five cases of lymphangioma comprising three intra-abdominal lymphangiomas and two unilateral axillary lymphangiomas presenting at one institution in Trinidad W.I. between 2005 and 2012 were examined. The presentations, location, workup, treatment, and outcome of these patients were studied. Conclusion. This paper discusses a range of extracervical lymphangioma cases seen at San Fernando General Hospital, Trinidad W.I. We report three intra-abdominal cases and the most common clinical presentations were abdominal pain and distension. Also two axillary cases were reported, which presented as painless axillary masses. The major concerns for excision of axillary lymphangioma by parents and surgeons were cosmesis and feasibility of complete resection without disruption of developing breast tissue and axillary vessels. We believe that ultrasound scan is very good at detection of the lesion, while CT is better at determining tumour content and planning for the operation. It is our opinion that complete surgical excision can be achieved.

Retroperitonealni limfangiom kao uzrok akutnog abdomena – prikaz slučaja

“…U otprilike polovine pacijenata prisutan je bol u trbuhu [3][4][5]9 . Druge moguće tegobe su mučnina, povraćanje, distenzija ili papabilna tvorba u trbuhu, konstipacija i dijareja [3][4][5]12 . Komplikacije, uključujući akutni abdomen, posljedica su infekcije ili intratumorskog krvarenja, intestinalne opstrukcije, volvulusa ili traumatske rupture 6 .…”

“…MR i CT bolje prikazuju karakteristike tvorbe i odnos prema susjednim strukturama te daju vrijedne podatke u preoperativnoj pripremi pacijenata. Mjerenjem gustoće ili intenziteta signala tekućine u cistama može se zaključiti je li sadržaj serozan, hilozan ili sangvinozan [12][13] . Iako je apendicitis najčešći razlog abdominalnog bola koji zahtijeva kiruršku intervenciju u djece školske dobi, ako izostaju klasični simptomi i znakovi treba bez odgađanja učiniti slikovne pretrage, počevši od ultrazvuka.…”

“…U većini slučajeva dijagnozu je moguće postaviti na temelju ultrazvučne pretrage, a za bolju procjenu lezije od koristi je MR [13][14]16 . Definitivna dijagnoza se postavlja patohistološkom analizom tkiva tumora 12,16 . Prognoza je nakon kompletne kirurške resekcije izvrsna 17 .…”

Anaesthetic Management of a Huge Oral Lymphangioma in a Neonate

“…75% of the cases were found in the head and neck, 15% are in axillary region. [2] Here we are reporting a huge lymphangioma of the tongue occupying the entire oral cavity.…”

Bladder Lymphangioma Treated by Holmium Laser: Extremely Rare Case Report

“…Typically, cystic lymphoid is formed in the neck and auxiliary with a prevalence of 70% and 20% respectively, and it is rarely seen in the urinary system. 3,4 The holmium laser has been used in urology since 1993 with a wavelength of 2140 nm absorbed by the tissue fluid. This property of helium leads to vaporization without deep coagulation and provides a safe margin.…”