Cephalometric Measurements in Patients with Pierre Robin Syndrome and Isolated Cleft Palate

Abstract

To compare craniofacial structure and growth, two standard lateral cephalograms of 35 children with Pierre Robin syndrome and 30 age and sex matched children with isolated cleft palate were taken at two different ages. The mean (SD) age of the children with Pierre Robin syndrome was 9.5 (3.0) years and of the children with isolated cleft palate 7.1 (1.1) years at the start of the follow up period. The follow up time in the first group was 4.3 (1.6) and in the second group 3.8 (2.7) years. There were no significant differences between the groups in the shape of the cranial base or the maxilla. The main differences were in the mandible, which showed more recession among those with Pierre Robin syndrome. There was a significant correlation between the shape of the maxilla and that of the mandible in that group, but not in the group with isolated cleft palate. During the follow up period there were no significant differences between the two groups in the rate of growth of the jaws. The association between the maxilla and the mandible (ss-n-sm) remained unchanged, or increased, or decreased with equal frequency in both groups. There was no catch up mandibular growth among the children with Pierre Robin syndrome.

Long-Term Results of Mandibular Distraction Osteogenesis with a Resorbable Device in Infants with Robin Sequence

“…13,29 Robin sequence infants might lack an intrinsic potential to grow out to values of healthy counterparts. [30][31][32][33][34] No studies have described the influence of mandibular distraction osteogenesis on craniofacial features in Robin sequence infants after longer follow-up. We demonstrated that, after a mean follow-up of 6.8 years, Robin sequence infants had a significantly shorter mandibular length compared with Robin sequence infants who did not undergo mandibular distraction osteogenesis.…”

Robin sequence: A European survey on current practice patterns

“…To determine the size and/or position of the mandible in the RS child, a number of measurement methods have been described in literature, such as the jaw index, plain x-rays, and computed tomgraphy scans (Figueroa et al 1991;Laitinen and Ranta 1992;van der Haven et al 1997;Vegter et al 1999;Daskalogiannakis et al 2001). In this survey, the majority of the respondents relied on clinical sight in the determination of an (ab)normal size and/or position of the mandible.…”

Three-Dimensional Assessment of Facial Development in Children With Pierre Robin Sequence

“…This deficit can be seen from the youngest to the oldest examined children. By visual analysis of the position of the Laitinen and Ranta 6 have reported some maxillary retrusion compared with healthy Scandinavian children using cephalometry. More precise information, however, is missing.…”