Cerebellopontine angle lipomas, multiple pigmented nevi, and temporal lobe hypoplasia: a new neurocutaneous syndrome?

Amonkar, P P; Patil, JR; Merchant, SE

doi:10.2214/ajr.169.5.9353474

Cited by 10 publications

(3 citation statements)

References 5 publications

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“…It is known that the severity of clinical signs is generally correlated with tumor size, so this patient may become clinically apparent at later stages if the lesions increase in size 27 . Several other asymptomatic cases have been reported in literature 16,22,27,28 .…”

Section: Discussionmentioning

confidence: 97%

Rare Bilateral Lipoma of the Internal Auditory Canals

2010

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About 10% of all intracranial tumors are localized in the cerebellopontine angle and in the internal auditory canal. Less than 2% of these are lipomas. Furthermore, it can be expected that lipomas in this position with a bilateral localization are exceedingly rare. We describe a 70-year-old-woman with lipomas in both internal auditory canals presented in the literature for the first time and include a detailed literature research.

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Section: Discussionmentioning

confidence: 97%

Rare Bilateral Lipoma of the Internal Auditory Canals

2010

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“…A total of 9 cases are summarized in Table 1, including 8 collected from the literature review and the case presented herein. [1][2][3][4][5][6][7] The cohort includes 6 male (67%) and 3 female (33%) patients. With regard to symptoms, 5 cases were found incidentally (56%), 2 patients experienced tinnitus (22%), 1 patient reported frontal headaches (11%), and 1 case was identified during autopsy (11%).…”

Section: Literature Reviewmentioning

confidence: 99%

“…Bilateral cerebellopontine angle (CPA) lipomas are an extremely rare condition; only 8 cases have been reported in the literature. [1][2][3][4][5][6][7] Here we report a case of asymptomatic bilateral CPA lipomas in a newborn, which were diagnosed incidentally during the workup for an occipital encephalocele. This is the first case of bilateral CPA lipomas in an infant as well as the first case with a coexisting intracranial anomaly.…”

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confidence: 99%

Bilateral cerebellopontine angle lipomas in an infant with encephalocele: illustrative case

Zhao,

Prather,

Tavakol

et al. 2023

Journal of Neurosurgery: Case Lessons

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BACKGROUND Bilateral cerebellopontine angle (CPA) lipomas are extremely rare. Herein the authors present a case of bilateral CPA lipomas in an infant along with a literature review of bilateral CPA lipomas. OBSERVATIONS A newborn girl was incidentally found to have bilateral CPA lipomas during the workup for an occipital encephalocele. The encephalocele was repaired primarily on day 2 after birth. The patient demonstrated no symptoms associated with the bilateral CPA lipomas. Eight cases of bilateral CPA lipomas were identified in the literature review and are summarized. Conservative management is the consensus strategy, given minimum growth of the tumor and the high risk of surgical intervention. LESSONS This is the first reported case of bilateral CPA lipomas in an infant as well as the first with a coexisting intracranial malformation. Intracranial lipomas share an extremely low growth rate and typically do not cause severe symptoms. The management of asymptomatic or mildly symptomatic bilateral CPA lipomas is usually conservative.

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