Characteristic imaging features of desmoplastic small round cell tumour

Arora, Vandan; Price, Anita P.; Fleming, Stephen E.; Sohn, Michael; Magnan, Heather; LaQuaglia, Michael P.; Abramson, Sara J.

doi:10.1007/s00247-012-2485-0

Cited by 53 publications

(68 citation statements)

References 24 publications

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“…Larger masses (>10 cm) may have a central area of low attenuation with heterogeneous contrast enhancement correlating with necrosis, old hemorrhage, and possibly fibrosis (Figs 11, 12) (70,75,78). Small punctate or amorphous calcifications are seen in at least 30% of cases (Fig 13) (70,75,78). Liver metastases and abdominal and retroperitoneal lymph nodes are hypoattenuating (Fig 13) (78).…”

Section: Diffuse Disease Desmoplastic Small Round Cell Tumormentioning

confidence: 93%

“…On cross-sectional images, the typical findings of DSRCT are multiple peritoneal, omental, and serosal masses without a clear organ of origin (67,70,75). The masses are most often round or ovoid and range in size from 3 to 22 cm, with an average size of 11.2 cm.…”

Section: Diffuse Disease Desmoplastic Small Round Cell Tumormentioning

confidence: 96%

“…Initially described by Gerald and Rosai (69) in 1989, about 300 cases of DSRCT have since been reported in the literature (68). DSRCT most often develops as a primary tumor of the peritoneal cavity but can also arise in other sites including pleura, bone, testes, or salivary glands (70,71).…”

Section: Diffuse Disease Desmoplastic Small Round Cell Tumormentioning

confidence: 97%

“…At CT, small masses demonstrate low attenuation (24-36 HU) with uniform enhancement after contrast agent administration (70). Larger masses (>10 cm) may have a central area of low attenuation with heterogeneous contrast enhancement correlating with necrosis, old hemorrhage, and possibly fibrosis (Figs 11, 12) (70,75,78).…”

Section: Diffuse Disease Desmoplastic Small Round Cell Tumormentioning

confidence: 98%

See 3 more Smart Citations

Solid Tumors of the Peritoneum, Omentum, and Mesentery in Children: Radiologic-Pathologic Correlation:From the Radiologic Pathology Archives

Em¹,

Dm²,

Am³

et al. 2015

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Intraperitoneal solid tumors are far less common in children than in adults, and the histologic spectrum of neoplasms of the peritoneum and its specialized folds in young patients differs from that in older patients. Localized masses may be caused by inflammatory myofibroblastic tumor, Castleman disease, mesenteric fibromatosis, or other mesenchymal masses. Inflammatory myofibroblastic tumor is a mesenchymal tumor of borderline biologic potential that appears as a solitary circumscribed mass, possibly with central calcification. Castleman disease is an idiopathic lymphoproliferative disorder that appears as a circumscribed, intensely enhancing mass in the mesentery. Mesenteric fibromatosis, or intra-abdominal desmoid tumor, is a benign tumor of mesenchymal origin associated with familial adenomatous polyposis. Mesenteric fibromatosis appears as a mildly enhancing, circumscribed solitary mass without metastases. Diffuse peritoneal disease may be due to desmoplastic small round cell tumor (DSRCT), non-Hodgkin lymphoma, or rhabdomyosarcoma. DSRCT is a rare member of the small round blue cell tumor family that causes diffuse peritoneal masses without a visible primary tumor. A dominant mass is typically found in the retrovesical space. Burkitt lymphoma is a pediatric tumor that manifests with extensive disease because of its short doubling time. The bowel and adjacent mesentery are commonly involved. Rhabdomyosarcoma may arise as a primary tumor of the omentum or may spread from a primary tumor in the bladder, prostate, or scrotum. Knowledge of this spectrum of disease allows the radiologist to provide an appropriate differential diagnosis and suggest proper patient management.

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Section: Diffuse Disease Desmoplastic Small Round Cell Tumormentioning

confidence: 93%

Section: Diffuse Disease Desmoplastic Small Round Cell Tumormentioning

confidence: 96%

Section: Diffuse Disease Desmoplastic Small Round Cell Tumormentioning

confidence: 97%

Section: Diffuse Disease Desmoplastic Small Round Cell Tumormentioning

confidence: 98%

See 2 more Smart Citations

Solid Tumors of the Peritoneum, Omentum, and Mesentery in Children: Radiologic-Pathologic Correlation:From the Radiologic Pathology Archives

Em¹,

Dm²,

Am³

et al. 2015

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“…The most common imaging finding of patients with intra-abdominal DSRCT was multiple peritoneal soft tissue masses, with a dominant mass in the retrovesical or rectouterine location in more than half of the cases. 2 All tumors show inhomogeneous enhancement on CT. Punctate area of calcification can be seen. MRI findings include lesions with hyperintense T2 -weighted signal and an isointense signal on T1-weighted sequences.…”

Section: Case Reportmentioning

confidence: 99%

Rare peritoneal tumour presenting as uterine fibroid

Kanthi

Sreedhar

Nair

2014

Int J Reprod Contracept Obstet Gynecol

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Intra‐abdominal omental mass as a desmoplastic round cell tumor: A rare case report

Bohara,

Jha,

Bhat

et al. 2023

Clinical Case Reports

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Key Clinical MessageDesmoplastic round cell tumor, though rare, must be taken into consideration as a differential diagnosis, thus aiding in early evaluation and changing the trajectory of the natural history of the disease condition, and improving the prognosis of patients.AbstractDesmoplastic small round cell tumor is a rare, aggressive tumor of mesenchymal origin with an incidence of 0.74 cases per million. We present a young adult with a periumbilical mass who was diagnosed as a desmoplastic round cell tumor and later was treated with exploratory laparotomy and resection of the tumor with no recurrence during a 6‐month follow‐up period.

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Characteristic imaging features of desmoplastic small round cell tumour

Cited by 53 publications

References 24 publications

Solid Tumors of the Peritoneum, Omentum, and Mesentery in Children: Radiologic-Pathologic Correlation:From the Radiologic Pathology Archives

Solid Tumors of the Peritoneum, Omentum, and Mesentery in Children: Radiologic-Pathologic Correlation:From the Radiologic Pathology Archives

Rare peritoneal tumour presenting as uterine fibroid

Intra‐abdominal omental mass as a desmoplastic round cell tumor: A rare case report

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