“…Carcinoma generally develops in the extrahepatic bile duct (26,32). Adenocarcinoma is the most common histology, squamous and undifferentiated carcinomas are also reported, but less frequently (24,31,33 (15,18). Analysis of ERCP studies in adults has shown abnormalities of the pancreatobiliary junction, which have provided clues to the etiology of the choledochal cysts (2,8,9).…”