Choledochal Cyst: Their clinical presentation, diagnosis and treatment in central Nepal: a retrospective study

Abstract

Background & Objectives:Choledochal cyst is a r ar e congenital malformation involving the cystic dilatation of intrahepatic and/ or extrahepatic bile duct .The estimated incidence is one in 1000 live birth in Asian population with female to male ratio 3:1. The objective of the study was to study the presentation, diagnosis, treatment and outcome of choledochal cyst in College of Medical Sciences, Bharatpur, Nepal Materials & Methods: A r etr ospective r eview of the r ecor ds of all the patients who were diagnosed as choledochal cyst and underwent medical or operative intervention in our hospital from January 2013-January 2015. Results: We analyzed ten cases of choledochal cyst. The condition commonly affected the age group of six to ten years with female preponderance (70%). Most common presenting symptom was pain abdomen (100%) and jaundice (50%). However classical triad of abdominal pain, jaundice, and an abdominal mass was not seen in any of the cases. Ultrasonography was diagnostic in all cases. Todani type I cyst was the most common type. Nine out of ten cases underwent complete cyst excision with cholecystectomy and Roux-en-Y hepaticojejunostomy without any major complication. Conclusion: Choledochal cyst is a clinical condition that is conveniently diagnosed on ultrasound and has a rewarding outcome if operated