BackgroundChoristomas consist of the proliferation of normal cells or tissue in an abnormal location. Oral choristomas are considered very rare.AimsThe present study aims to report a case of dorsal tongue surface cartilaginous choristoma, with emphasis on its clinical and histopathological features.Case ReportA 72‐year‐old woman attended a dental office with a chief complaint of a persistent tongue lesion. The patient reported that the lesion grew slowly for about 3 months, with no trauma history in the region. An intraoral examination revealed a nodular lesion on the dorsal tongue surface, normal mucosa coloration, firm consistency and sessile implantation, measuring approximately 1.5 cm in diameter. Based on the clinical examination, a diagnosis hypothesis of a granular cell tumour was considered, and an excisional biopsy was performed for confirmation. Given the microscopic findings, the histopathological diagnosis confirmed a cartilaginous choristoma. The patient has been under follow‐up for 12 months, with no signs of relapse.ConclusionThis case highlights the importance of clinical and histopathological findings for the correct diagnosis and treatment of oral choristoma.