Chordoma in a child presenting as unilateral proptosis with high serum alpha‐fetoprotein

Abstract

A 14-month-old girl with intracranial chordoma involving the left orbit, paranasal sinuses, nasal cavity and hard palate presented with unilateral proptosis. The serum ufetoprotein was markedly elevated. Such intracranial tumors in infancy tend to be aggressive and have a great tendency for rapid growth as well as distant metastases.