Churg–Strauss syndrome presenting as an abdominal mass in a non-asthmatic child

Hamdan, Mohamed A.; Al-Rumaithi, Sareea; Tolaymat, Naser; Ionescu, Gabriel; Al-Ashari, Moueid; El-Teraifi, Hassan

doi:10.1179/146532807x245724

Cited by 4 publications

(2 citation statements)

References 10 publications

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“…The mortality rate of CSS is approximately 5% in adults (8) and is significantly worse in children, at 15.9% (7/44). In the past four years, 2 of the 11 pediatric CSS patients died due to pulmonary abscess and sepsis despite treatment with immunosuppressive drugs and intravenous immunoglobulin (1,9). The other predominant causes of death include heart failure, renal failure, cerebral failure, and gastrointestinal perforation/hemorrhage.…”

Section: Discussionmentioning

confidence: 99%

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A possible case of Churg-Strauss syndrome in a 9-year-old child

Liu¹,

Xu²,

Chen³

et al. 2012

Clinics

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Section: Discussionmentioning

confidence: 99%

“…It typically occurs in conjunction with a history of asthma, eosinophilia, pulmonary infiltrates, and vasculitis, but cases without asthma have also been reported (1-2). CSS has rarely been reported in pediatric patients.…”

Section: Introductionmentioning

confidence: 99%

A possible case of Churg-Strauss syndrome in a 9-year-old child

Liu¹,

Xu²,

Chen³

et al. 2012

Clinics

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Eosinophilic granulomatosis with polyangiitis without respiratory symptoms or asthma in an adolescent: case report and literature review

et al. 2017

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Eosinophilic granulomatosis with polyangiitis (EGPA), also known as Churg-Strauss syndrome, is a systemic necrotizing vasculitis of the small and medium vessels. It is primarily associated with respiratory conditions such as asthma and sinusitis as well as eosinophilia, neuropathy, pulmonary infiltrates, and vasculitis. EGPA is extremely rare in the pediatric age group, and respiratory system disorders are usually predominant in EGPA patients. A 14-year-old boy presented with rash and severe extremity pain. He had eosinophilia, and electroneuromyography demonstrated sensorimotor polyneuropathy. His skin biopsy revealed necrotizing eosinophilic vasculitis and eosinophilic panniculitis. Although he had no respiratory symptoms or history of asthma, prominent pulmonary involvement was evident on thoracic MRI. After treatment, his complaints of pain improved but mild neuropathy persisted. After 4 years of follow-up, he had minimal hypoesthesia in his right hand but had not experienced any relapses. This case highlights the fact that in cases suspected of EGPA, even without respiratory symptoms or asthma, detailed imaging should be performed for a definitive diagnosis. In addition, mild neurological findings may persist despite treatment in EGPA. The relevant literature on EGPA, with specific reference to pediatric cases, is reviewed.

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Clinical presentation of Churg–Strauss syndrome in children

Razenberg

Heynens

Vries

et al. 2012

Respiratory Medicine Case Reports

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Churg–Strauss syndrome is an uncommon multisystem disorder characterized by asthma, eosinophilia and vasculitis. We report on a 12-year-old boy with asthma and deterioration of his general condition, who was eventually diagnosed with an ANCA-negative Churg–Strauss syndrome. The propositus included, 50 cases of childhood Churg–Strauss syndrome have been reported. The patient characteristics and clinical characteristics of these children are summarized. The respiratory tract is most frequently involved with pulmonary infiltrates, asthma and sinusitis. Early recognition of childhood Churg–Strauss syndrome is important as delayed diagnosis can lead to severe organ involvement, and possible fatal outcome.

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Churg–Strauss syndrome presenting as an abdominal mass in a non-asthmatic child

Cited by 4 publications

References 10 publications

A possible case of Churg-Strauss syndrome in a 9-year-old child

A possible case of Churg-Strauss syndrome in a 9-year-old child

Eosinophilic granulomatosis with polyangiitis without respiratory symptoms or asthma in an adolescent: case report and literature review

Clinical presentation of Churg–Strauss syndrome in children

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