Clinical Presentation of Chiari I Malformation and Syringomyelia in Children

Pindrik, Jonathan; Johnston, James M.

doi:10.1016/j.nec.2015.06.004

Cited by 31 publications

(21 citation statements)

References 18 publications

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“…59 The clinical presentation of pediatric C1D differs from that of adults, particularly for very young children presenting with, for example, sleep apnea and feeding difficulties (►Table 1). 5,60,61 Compared with adults, children have generally a shorter duration of symptoms.…”

Section: Clinical Findingsmentioning

confidence: 99%

Chiari Type 1 Deformity in Children: Pathogenetic, Clinical, Neuroimaging, and Management Aspects

et al. 2016

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Our understanding of cerebellar tonsillar herniation evolved over time and nowadays various pathomechanisms have been proposed. Causes of tonsillar herniation share a discrepancy between content (fore- and hindbrain) and container (supratentorial cranial vault, posterior fossa), may be associated with abnormalities of the craniocervical junction, and may have a developmental or acquired nature. In tonsillar herniation, the hindbrain is not malformed but deformed. Accordingly, "Chiari type 1 deformity," not "Chiari type 1 malformation" is the correct term to characterize primary tonsillar herniation. Chiari type 1 deformity is commonly seen in pediatric neurology, neuroradiology, and neurosurgery and may have various clinical presentations depending on patient age. In addition, Chiari type 1 deformity is increasingly found by neuroimaging studies as an incidental finding in asymptomatic children. An accurate and reliable selection of patients based on clinical and neuroimaging findings is paramount for the success of neurosurgical treatment. Future studies are needed to provide selection criteria with a higher sensitivity and specificity.

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Section: Clinical Findingsmentioning

confidence: 99%

Chiari Type 1 Deformity in Children: Pathogenetic, Clinical, Neuroimaging, and Management Aspects

et al. 2016

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“…Some controversy remains whether syringomyelia in patients with CID is a strict surgical indication, since the medical literature has several descriptions of spontaneous resolution of the syrinx in such cases or at least stability/ absence of progression, even in cases of large syringomyelic cavities. 38,39 Magge et al studied 48 children with an idiopathic syrinx and found out that 91% of them remained clinically asymptomatic, stable or improved over a mean follow-up of 23.8 months. 40 In those who had follow-up imaging, 87.5% remained radiologically stable or the syrinx reduced over time, with no apparent correlation between changes in size of the syrinx and evolution of symptoms.…”

Section: Clinical Questions 1) What Is the Definition And Best Nomencmentioning

confidence: 99%

Management of Chiari I deformity in Children and Adolescents: A report from the Consensus Taskforce of the Brazilian Society of Pediatric Neurosurgery

Santos

Furlanetti

Canheu

et al. 2020

Arquivos Brasileiros de Neurocirurgia: Brazilian Neurosurgery

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Much controversy remains on the current management of Chiari I deformity (CID) in children, with many clinical, surgical and ethic-legal implications. The Brazilian Society of Pediatric Neurosurgery (SBNPed, in the Portuguese acronym) has put together a panel of experts to analyze updated published data on the medical literature about this matter and come up with several recommendations for pediatric neurosurgeons and allied health professionals when dealing with CID. Their conclusions are reported herein, along with the respective scientific background.

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“…It is often a result of CVJ developmental disorders, where the bone tissue remains normal, such as basioccipital (clivus) hypoplasia, atlas hypoplasia, occipital condyle hypoplasia, achondroplasia, or an incomplete ring of C1 with spreading of the lateral masses and atlanto-occipital assimilation. Chiari malformation is often associated with basilar invagination and other CVJ abnormalities and may be present in up to 33-38 % of patients [2]. In a recent retrospective study of patients with Chiari malformation who underwent surgery, 13 % (46 out of 350) had associated basilar invagination, and 67 % (31 out of 46) of those patients had a ventral compression in the foramen magnum [3].…”

Section: Basilar Invagination Basilar Impression and Platybasia: Dementioning

confidence: 99%

Basilar Invagination, Basilar Impression, and Platybasia: Clinical and Imaging Aspects

Pintér

McVige

Mechtler

2016

Curr Pain Headache Rep

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The congenital and acquired deformities of the craniovertebral junction (CVJ), such as basilar invagination, basilar impression, or platybasia, can present in the form of slowly progressive or acute neurologic deterioration. In many cases, an insidious headache is the only symptom and can be a diagnostic challenge for the neurologist. Proper imaging studies as well as recognizing often associated neurologic or systemic conditions are required for early diagnosis and effective therapy. In the current report, the primary focus will be on clinical aspects of these CVJ abnormalities; the pathologic and radiologic aspects, such as developmental and pathophysiologic background or radiographic analysis, will be discussed briefly, confined to clinically relevant data.

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Clinical Presentation of Chiari I Malformation and Syringomyelia in Children

Cited by 31 publications

References 18 publications

Chiari Type 1 Deformity in Children: Pathogenetic, Clinical, Neuroimaging, and Management Aspects

Chiari Type 1 Deformity in Children: Pathogenetic, Clinical, Neuroimaging, and Management Aspects

Management of Chiari I deformity in Children and Adolescents: A report from the Consensus Taskforce of the Brazilian Society of Pediatric Neurosurgery

Basilar Invagination, Basilar Impression, and Platybasia: Clinical and Imaging Aspects

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