Clinical Study of Twenty-Three Cases of Ebstein's Anomaly of the Tricuspid Valve

Abstract

The clinical findings in 23 cases of Ebstein's anomaly are presented, together with a discussion of the diagnostic and surgical aspects of this defect. Attention is again drawn to the frequent occurrence of the Wolff-Parkinson-White electrocardiographic pattern in this anomaly.

A Comparison of the Clinical, Haemodynamic and Angiographic Features in Right Ventricular Endomyocardial Fibrosis and Ebstein’s Anomaly of the Tricuspid Valve

“…Central cyanosis was present in 37% of our EATV patients as has been the experi ence o f other workers [5], However, this find ing was equally common in the RVEMF group; presumably the elevated right atrial pressure leads to a right to left shunt across the foramen ovale [6]. All 4 patients with cyanosis had a right atrial pressure greater than 17 mm Hg.…”

Clinical Use of Electrocardiography in Adults With Congenital Heart Disease

“…59 In the absence of ventricular preexcitation, the QRS axis is generally normal although occasionally leftward. 60 Q waves are noted in lead V 1 in about 50% of patients and may extend as far as lead V 4 . 61,62 T-wave inversion in leads V 1 to V 4 is common.…”

Ebstein’s Anomaly

“…57 Successful operative intervention for regurgitation of the tricuspid valve in patients with the anomaly was first described in 1962; the valve was replaced. 58 The initial publication on patients with Ebstein's anomaly undergoing tricuspid valve replacement reported a surgical mortality of 54%.…”

“…49 Similar high early mortality and unsatisfactory late results for tricuspid valve repair by the methods available at that time were described. 57,59 Between April 1972 and January 2005, 540 consecutive patients with Ebstein's anomaly were operated on at Mayo Clinic Rochester. The age at operation ranged from 2 months to 79.1 years (median, 20 years).…”