Coarctation of aorta with right aortic arch. Report of surgical correction in 2 cases: one with associated anomalous origin of left circumflex coronary artery from the right pulmonary artery.

Abstract

Two patients with right aortic arch, anomalous left subclavian artery, and coarctation of the aorta, have had operations for the relief of coarctation, successful in one but only partially successful in the other: in one case, a 'dacron' patch was inserted into the narrowed segment, but a mild recurrence of coarctation was found a year later; in the other, the proximal segment of the anomalous left subclavian artery was usedfor the repair, with complete relief of the coarctation, both immediately and at late follow-up.The first case had multiple associated congenital abnormalities, including anomalous origin of the left circumflex coronary artery from the right pulmonary artery, which was also corrected surgically: this anomaly has only been recorded once hitherto. The second had facial haemangiomata and a small ventricular septal defect.Four previously reported cases of coarctation and right arch are reviewed. These 6 cases are considered in the light of current views on the development and classification of aortic arch anomalies.

Hemangioma, supraumbilical midline raphé, and coarctation of the aorta with a right aortic arch: Single causal entity?

“…The patient at 5 months: multiple hemangiomas on right cheek, eyelids, forehead, lip, nose, chin, and ear. Zelikovsky et al, 1974;Honey et al, 1975;Edelman et al, 1983;Vaillant et al, 1988;Reese et al, 19931. Of these 10, hemangiomas were present in 3 cases.…”

Haemangioma of the head and neck with subglottic involvement and atypical coarctation

“…Rarely, they are associated with subglottic haemangiomas which may precipitate an acute respiratory emergency 1,2 . A number of reports have documented an association between head and neck haemangiomas and anomalies of the major blood vessels of the head and neck region 3–7 . In some, the haemangiomas have been associated with atypical anatomy of the coarctation and a disproportionately higher incidence of right‐sided coarctation of the aorta (Table 1).…”

“…In some, the haemangiomas have been associated with atypical anatomy of the coarctation and a disproportionately higher incidence of right‐sided coarctation of the aorta (Table 1). Right‐sided coarctation as an isolated cardiac anomaly is uncommon with a limited number of cases being reported in the literature 5 . It is thought that the relative length and position of the arterial duct in a right aortic arch favours flow round the arch and through the isthmus rather than through the duct.…”

Right Aortic Arch and Coarctation: A Rare Association

“…The combination of right aortic arch and coarctation is exceedingly rare; however, there have been a number of reports, beginning as early as the late 1960s 5–8 . A more recent review of cases of right aortic arch associated with vascular obstruction noted a number of cases in the literature; 3 however, all of those with coarctation were single‐case reports, save 1 with 2 cases 8 . More recent reports have also consisted of descriptions of 1 or 2 cases, occasionally in association with other anomalies or syndromes 9–12 .…”

“…[5][6][7][8] A more recent review of cases of right aortic arch associated with vascular obstruction noted a number of cases in the literature; 3 however, all of those with coarctation were single-case reports, save 1 with 2 cases. 8 More recent reports have also consisted of descriptions of 1 or 2 cases, occasionally in association with other anomalies or syndromes. [9][10][11][12] Finally, an ideal surgical approach for these patients has been defined through only a small number of cases.…”