Cochlear implantation in patients with Cogan's syndrome: a review of four cases

Abstract

Cogan's syndrome is a rare disorder that is characterized by a rapid onset of bilateral severe sensorineural hearing loss associated with vertigo and tinnitus, ocular involvement (most commonly an interstitial keratitis) and variable systemic symptoms. We review our experience with four cases treated in our department. We describe their symptoms, the evolution of their disease, the diagnosis, and the radiological investigations with computed tomography and/or magnetic resonance imaging. When medical treatment with corticosteroids failed and no benefit could be obtained with hearing aids at each patient's end stage, all patients received a cochlear implant with excellent results. The considerations for implantation in these patients are discussed.

Complete restoration of auditory impairment in a pediatric case of Cogan's syndrome: Report of a rare case with long-term follow-up and literature review

“…Cochlear implantation could be suggested in profound hearing loss with good results in few cases [3,[11][12][13].…”

Long-Term Evaluation of Cochlear Implantation in Cogan Syndrome

“…Two of these patients achieved great scores in speech perception. In the same year, 4 more cochlear implant recipients with Cogan syndrome enjoyed satisfactory hearing rehabilitation [9] . Pasanisi et al [6] described 5 patients with Cogan syndrome with excellent hearing outcomes after cochlear In the PTA the mean hearing threshold of 0.5, 1, 2 and 4 kHz is presented.…”

“…Previously reported cases of cochlear implantation in Cogan syndrome have either referred to isolated cases or focused on a follow-up lasting up to 12 months [6,8,9] . These data are not sufficient to form a global approach to cochlear implantation in this rare but interesting subpopulation.…”

Cogan's syndrome is a new nosological entity in the current classification of systemic vasculitides: A clinical case and a review of literature

“…Перспективной стратегией реабилитации пациентов с СК является кохлеарная имплантация, демонстрирую-щая хорошие результаты [11,18,[45][46][47]. При вестибуляр-ных жалобах применяют симптоматическое лечение.…”