Communicating bronchopulmonary foregut malformation: Volume change of the affected lung after birth

Kobayashi, Hisato; Miyakoshi, Kei; Koinuma, Goro

doi:10.1002/ppul.24296

Cited by 3 publications

(2 citation statements)

References 4 publications

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“…Two additional case reports described rare fistulous connections involving the GI and respiratory systems. Kobayashi et al 20 bronchus was visualized endoscopically. The patient was initially stable but progressed to respiratory failure at age 5 months of age.…”

Section: Anatomic Lung Airway and Vascular Malformationsmentioning

confidence: 99%

“…Two additional case reports described rare fistulous connections involving the GI and respiratory systems. Kobayashi et al 20 reported communicating bronchopulmonary foregut malformation presenting with lung volume change shortly after birth. At 3 months of age, communication between the lower esophagus and right mainstem bronchus was visualized endoscopically.…”

Section: Introductionmentioning

confidence: 99%

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Pediatric pulmonology 2019 year in review: rare and diffuse lung disease

Gower

Vece

2021

Pediatric Pulmonology

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Pediatric Pulmonology publishes original research, review articles, and case reports on topics related to a wide range of children's respiratory disorders. Here we review manuscripts published in 2019 in this journal and others on (1) anatomic lung, airway, and vascular malformations, (2) children's interstitial lung disease, and (3) primary ciliary dyskinesia and non-cystic fibrosis bronchiectasis.

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Section: Anatomic Lung Airway and Vascular Malformationsmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

Pediatric pulmonology 2019 year in review: rare and diffuse lung disease

Gower

Vece

2021

Pediatric Pulmonology

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Computed tomography findings of communicating bronchopulmonary foregut malformation: a retrospective study of 18 patients

Han

Huang

et al. 2023

Pediatr Radiol

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Right esophageal lung with associated pulmonary vascular anomaly: A rare case report

Hailu,

Abrar

et al. 2023

International Journal of Surgery Open

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Introduction and Importance Congenital bronchopulmonary foregut malformation (CBPFM) is a rare anomaly in which either a lung, a lung lobe or a segment has a patent congenital communication to the upper gastrointestinal tract. In esophageal lung, an anomalous main bronchus arises from the esophagus rather than the trachea. Case presentation A male neonate was admitted with respiratory distress immediately following birth. Radiographic evaluation included chest radiograph, chest Ultrasound, chest CT and an upper gastrointestinal (GI) contrast study. A completely opaque right hemithorax was initially visualized and identified as esophageal lung with associated anomalous partial systemic arterial supply and venous drainage. A right posterolateral thoracotomy with pneumonectomy of the hypoplastic lung was performed. However, the patient died of respiratory failure on the first postoperative day. Clinical discussion Esophageal lung is an extremely rare form of CBPFM in which a main stem bronchus, usually the right one, is abnormally connected to the esophagus. The diagnosis is suggested by chest x-ray and confirmed by upper GI contrast study, which is also available in resource-poor settings. A CT scan with 3D volume rendered images can make a diagnosis, although difficulties remain. Pneumonectomy is the preferred treatment for most patients. Conclusion Esophageal lung is a rare congenital abnormality with few reported cases. Radiologists and pediatricians should have a high index of suspicion for this anomaly in cases of neonatal respiratory distress and a persistently opacified lung with focal air bronchogram(s) and pursue a timely confirmatory contrast study. Highlights

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Communicating bronchopulmonary foregut malformation: Volume change of the affected lung after birth

Cited by 3 publications

References 4 publications

Pediatric pulmonology 2019 year in review: rare and diffuse lung disease

Pediatric pulmonology 2019 year in review: rare and diffuse lung disease

Computed tomography findings of communicating bronchopulmonary foregut malformation: a retrospective study of 18 patients

Right esophageal lung with associated pulmonary vascular anomaly: A rare case report

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