Complete Susac syndrome in a 22-year old male in Colombia: Case report and a review of the literature

Introduction: Susac syndrome is a disease with autoimmune microangiopathic etiology of vascular endothelia that causes occlusion of arterial branches. Due to its high diagnostic complexity, it cannot be detected at the onset of the syndrome because most patients do not present the characteristic triad at a certain time, they start their picture with neurological manifestations which implies several differential diagnoses. Aim: To describe the correct management of Susac Syndrome based on the main diagnostic criteria and the efficacy of pharmacological treatment. Methods: A literature review study of articles from 2017 to 2022 on Susac syndrome was conducted in the following databases: Scopus, SciELO, Pubmed, Cochrane and Lilacs. Results: This disease is characterized by the presence of a pathognomonic triad of encephalopathy, sensorineural hearing loss and retinal arterial occlusion. Consequently, it is vital to use different diagnostic methods: laboratory data, imaging studies and audiometry. Treatment regimens have been proposed, establishing corticosteroids and immunomodulators as the first line of treatment. When considering pharmacological treatments, not only the severity of SS must be contemplate but also the presence of comorbidities and characteristics according to each patient in order to define the appropriate pharmacological scheme for each patient. Conclusions: Audiometric examinations are considered fundamental for the diagnosis since sensorineural hearing loss can be evidenced in low and medium frequencies, it is important to perform surgical interventions with the purpose of avoiding the progression of the syndrome.

show abstract

Management of Susac Syndrome

Chamba

Garzón

Jiménez

et al. 2022

Salud, Ciencia y Tecnología

View full text Add to dashboard Cite

show abstract

scite is a Brooklyn-based organization that helps researchers better discover and understand research articles through Smart Citations–citations that display the context of the citation and describe whether the article provides supporting or contrasting evidence. scite is used by students and researchers from around the world and is funded in part by the National Science Foundation and the National Institute on Drug Abuse of the National Institutes of Health.

Contact Info

customersupport@researchsolutions.com

10624 S. Eastern Ave., Ste. A-614

Henderson, NV 89052, USA

This site is protected by reCAPTCHA and the Google Privacy Policy and Terms of Service apply.

Blog Terms and Conditions API Terms Privacy Policy Contact Cookie Preferences Do Not Sell or Share My Personal Information

Made with 💙 for researchers

Part of the Research Solutions Family.

Complete Susac syndrome in a 22-year old male in Colombia: Case report and a review of the literature

Cited by 1 publication

References 7 publications

Management of Susac Syndrome

Management of Susac Syndrome

Contact Info

Product

Resources

About