Complications of Parkes Weber Syndrome

Abstract

The article presents a clinical case of congenital arteriovenous dysplasia – Parkes Weber syndrome of the lower extremities. The features of its clinical picture and the difficulties of diagnosis are described. It is emphasized that Parkes Weber syndrome is a rare congenital disease of the vascular system, in some cases with the absence of its typical clinical manifestations and combined with other pathologies of the veins.

Pediatric Limb Asymmetry: A Unique Presentation of Angioosteohypertrophic Syndrome

“…Severe forms may involve additional symptoms such as pain, warmth, and pulsations in the affected limb [ 12 ]. Complications of the syndrome can include bleeding, skin infections, thromboses, and heart failure [ 5 ].…”

“…It is characterized by the presence of a predominantly arteriovenous vascular malformation in a limb, resulting in disproportionate limb growth [ 3 ]. In contrast to Klippel-Trenaunay syndrome, individuals with PWS exhibit arteriovenous malformations featuring abnormal connections between the arteries and veins within the affected limb, potentially leading to cardiac insufficiency [ 4 , 5 ]. Management approaches, akin to those for Klippel-Trenaunay syndrome, primarily involve symptomatic treatment [ 1 ].…”