Coronary artery fistula (CAF) is known be a rare defect of coronary artery. When there is an abnormal pre-capillary communication between single or multiple branches of the coronary artery and any of the cardiac chambers or great vessels, it is designated as CAF. It can be found in both congenital and acquired form. Congenital origin of fistula occupies higher percentage compared to the acquired one. A wide variety of imaging modalities have been lunched to provide the best possible way to access and treat the defect. With regard to the assessment of the coronary artery fistula, trans-thoracic Doppler echocardiography and multi-slice CT (MSCT) angiography have commendable role, however, MSCTA comes in the leading position.