Medulloblastomas are WHO grade 4 embryonal neuroepithelial tumors that typically occur in the posterior fossa in the pediatric population. They represent 68% of embryonal tumors. The study of congenital cases is scarce due to the rarity of reported patients. There is also no specific bibliography, however histologically and molecularly they can be classified. On the other hand, due to the young age of these patients, they are difficult to manage and have a higher risk of complications in the treatment. In addition to this, patients are born with alterations in the development of the central nervous system due to chronic intracranial hypertension caused by said tumor and have little functional development. The objective of this study is to teach us to recognize the diagnosis early, the evolution of the disease to lead to better treatment for these patients in the future.