Congenital cholesteatoma isolated to the mastoid presenting as stricture of the external auditory canal

Nagato, Toshihiro; Otaka, Ryuki; Wada, Tetsuji; Kanai, Naoki; Harabuchi, Yasuaki

doi:10.1016/j.ijporl.2012.02.032

Cited by 7 publications

(6 citation statements)

References 10 publications

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“…Fourteen articles were included in this review. [2][3][4][5][6][7][8][9][10][11][12][13][14][15] To the best of our knowledge, the total number of cases of cholesteatoma isolated in the mastoid region to be reported in the literature, regarded 23 patients (Table 1). All the papers analyzed described cases of isolated mastoid cholesteatoma that presented a congenital origin.…”

Section: Resultsmentioning

confidence: 99%

Isolated Congenital Mastoid Cholesteatoma with no Involvement of Aditus Ad Antrum and Middle Ear

Pace

Iannella

Rossetti

et al. 2021

Clin Med Insights Case Rep

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Cholesteatoma is a non-neoplastic, keratinized squamous epithelial lesion that affects the temporal bone. The middle ear is the most frequent, while the isolated cholesteatoma of the mastoid is rare. The aim of this study was to describe a rare case of isolated mastoid cholesteatoma with no involvement of aditus ad antrum and middle ear including a literature review of the topic. This case report describes the case of a 58 years old female with a cholesteatoma isolated in the mastoid region, evidenced by imaging (computer tomography and magnetic resonance). A mastoidectomy was performed: mastoid process was completely involved, but antrum was not reached. Moreover, it reached the soft tissue of stylomastoid foramen as well as the posterior belly of the digastric muscle. In the literature few articles described cases of cholesteatoma isolated in the mastoid region. Research was conducted using PubMed and reference list and there were considered only reports about cholesteatoma exclusively located in the mastoid process without involvement of antrum or middle ear. Fourteen articles were included in this review, with a total number of 23 cases of cholesteatoma isolated in the mastoid region. All papers analyzed reported the cases of isolated mastoid cholesteatoma that presented a congenital origin. Its diagnosis is difficult, therefore, imaging evaluation is mandatory and surgery is the treatment of choice. Mastoid cholesteatomas without involvement of aditus ad antrum and middle ear are rare and only 23 cases are reported in literature. Our case is in line with all clinical and diagnostic features of this rare disease, but it is the only one that evidenced an exposure of the soft tissue of stylomastoid foramen as well as the posterior belly of the digastric muscle. The treatment of choice was the surgical one, avoiding damaging of important anatomo-functional structure.

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Section: Resultsmentioning

confidence: 99%

Isolated Congenital Mastoid Cholesteatoma with no Involvement of Aditus Ad Antrum and Middle Ear

Pace

Iannella

Rossetti

et al. 2021

Clin Med Insights Case Rep

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“…The incidence of CC is estimated to be between 4 and 24% of all cholesteatomas in children, but presentations in adults are common and should not be overlooked [3,6,[11][12][13][14]. Although small middle ear lesions are sometimes set apart from petrous bone cholesteatomas, they should be taken as seriously as they grow and will eventually cause much damage [9,12,14,15]. A diagnosis of CC should always be considered in patients presenting with otological symptoms with no previous history of discharge or infectious processes.…”

Section: Discussionmentioning

confidence: 99%

“…This is consistent with the previously reported series (60-100%). However, in 4 cases the ossicular chain was eroded with no hearing loss and in 2 cases the otic capsule was eroded with no sensorineural loss [3,4,6,9,12,17,18]. Discharge was the second commonest presentation (51.2%).…”

Section: Discussionmentioning

confidence: 99%

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Congenital Cholesteatoma: The Silent Pathology

Mostafa¹,

Fiky²

2018

ORL

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Background: Congenital cholesteatomas (CC) arise from epithelial remnants around the petrous bone. They enlarge gradually causing progressive destruction and functional damage to the ear and surrounding structures. Because of their insidious course, most patients are misdiagnosed and present late with complications. Methods: This is a retrospective study of 41 cases diagnosed as CC and followed up for 2 years. All patients underwent full audiological evaluation and a radiological study (CT, MRI). Results: The male:female ratio was 2.3: 1, and the mean age was 30.89 years. The mean delay before presentation was 13 months. The commonest presentations in order of frequency were: discharge (60.9%), hearing loss (51.2%), facial paralysis (31.7%) and intracranial complications (31.7%). Forty patients were treated surgically by a variety of approaches depending on the extensions and functional status. The facial nerve was decompressed in 9 cases and cable grafted in 4. Two cases underwent VII-XII anastomosis later on. Conclusion: CC present with a myriad of clinical manifestations and should be suspected in all patients with unexplained otological signs and symptoms. They must be completely excised and the functional status of the ear rehabilitated either immediately or later. Follow-up must be indefinite as they have a high recurrence rate.

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“…They also mentioned that, including their case, only four cases till that time presented with mastoid pain or swelling [ 13 ]. Another presentation of mastoid congenital cholesteatoma mentioned in the literature was a stricture in the external auditory canal with intact tympanic membrane [ 14 ].…”

Section: Discussionmentioning

confidence: 99%

Congenital Cholesteatoma Localized to the Mastoid Cavity and Presenting as a Mastoid Abscess

Tabook

Tawab

Gopal

2015

Case Reports in Otolaryngology

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Introduction. Congenital cholesteatoma is a pearly white mass that rarely originates from the mastoid process. Case Report. A 21-year-old male patient presented to our department with severe right mastoid pain and postauricular fluctuant swelling for 23 days. There was no preceding history of ear complaints and examination showed a normal right ear drum. Emergency exploration of the mastoid process was done on the same day and revealed localized cholesteatoma limited only to the mastoid cavity. Conclusion. Despite a rarity, the mastoid process should be always put in mind as a site of origin for congenital cholesteatoma.

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Congenital cholesteatoma isolated to the mastoid presenting as stricture of the external auditory canal

Cited by 7 publications

References 10 publications

Isolated Congenital Mastoid Cholesteatoma with no Involvement of Aditus Ad Antrum and Middle Ear

Isolated Congenital Mastoid Cholesteatoma with no Involvement of Aditus Ad Antrum and Middle Ear

Congenital Cholesteatoma: The Silent Pathology

Congenital Cholesteatoma Localized to the Mastoid Cavity and Presenting as a Mastoid Abscess

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