Congenital cyst of the pancreas in a newborn

Short Communication. Prenatal detection of a congenital pancreatic cyst and Beckwith–Wiedemann Syndrome

“…To the best of our knowledge, only three other cases have been detected prenatally by ultrasound scanning and ours is thus the fourth (Baker et al, 1990;Hopper et al, 1979;Fleet et al, 1993). Unlike pseudocysts of post-traumatic or post-inflammatory origin, true congenital cysts are lined by an epithelial layer.…”

“…The right upper quadrant location of the mass led us to suspect an intestinal duplication or choledocal cyst, but the pancreatic nature of the lesion could not be determined. It is actually extremely difficult to distinguish a pancreatic cyst from other intra-abdominal cystic masses, i.e., biliary tract lesion such as choledocal cysts, gastrointestinal obstructions, gastrointestinal duplication cysts, or mesenteric cysts (Fleet et al, 1993). Moreover, the precise nature of these lesions is often difficult to determine sonographically after birth, and in our particular case, we had to use computed tomography and upper gastrointestinal series to reveal the pancreatic location of the cyst.…”

How to differentiate congenital pancreatic cysts and cystic pancreatic teratomas?

“…The less invasive option in this situation is to perform a gastrocystostomy or duodenocystostomy [2,7,[24][25][26]. Alternatively, other surgeons choose to perform a cysto-jejunostomy by the Roux-en-Y technique with good results [2,3,14,16,20,30,33]. The present cases show that laparoscopic removal is a viable treatment option for congenital pancreatic cysts and pancreatic teratomas in infants, with minimal post-operative pain, minimal scaring, and short hospital stay [4,35].…”

“…Clinical, imaging findings, treatment, and outcomes of 33 other congenital pancreatic cysts reported in the literature are summarized in Table 1 [1,2,4,7,. Eleven of them were diagnosed prenatally [1,[13][14][15][16][17][18][19][20]36]. Clinical, imaging findings, treatment, and outcomes of 11 pancreatic teratomas in children are summarized in Table 2 [12,[37][38][39][40][41][42][43][44][45].…”

A large congenital pancreatic cyst mimicking a macrocytic lymphatic malformation

“…The neonate expired shortly after delivery due to respiratory failure from pulmonary hypoplasia . Twenty-one reports of prenatally diagnosed lesions have since been published [6] , [7] , [8] , [9] , [10] , [11] , [12] , [13] , [14] , [15] , [16] , [17] , [18] , [19] , [20] , [21] , [22] , [23] , [24] and ours provides the 22nd. These cases primarily describe CPCs as simple-appearing, unilocular cysts of various sizes in the upper abdomen.…”