Congenital cystic lesions of the lung

Left Upper Lobectomy for Congenital Lobar Emphysema in a Low Weight Infant

“…In literature 12–20% concomitant CHD or vascular slings have been reported. Therefore, many studies recommend the performance of echocardiography during the differential examination [1, 3, 4]. In our case echo revealed only the presence of a PDA.…”

“…CLE occurs in 1 case per 20–30 thousand births [2]. The etiology of congenital lobar emphysema is idiopathic in half of cases, whereas the other 50% have several mechanisms proposed to explain the air-trapping, which can be divided into intrinsic and extrinsic subtypes [3]. …”

Refractory tension pneumothorax as a result of an internally displaced thoracoamniotic shunt in an infant with a congenital pulmonary airway malformation

“…CTM are a heterogeneous group of rare malformations, which include CPAMs, bronchogenic cysts, pulmonary sequestrations and congenital lobar emphysema and other cystic lesions 1 2. With improvement in ultrasound imaging technology, these lesions are often visualised antenatally 6.…”

“…As antenatal ultrasound scans have become a part of standard prenatal care, cystic lung lesions are sometimes identified, and can represent a range of congenital thoracic malformations (CTMs), including congenital pulmonary airway malformations (CPAMs) 1 2. While many of these malformations are well tolerated in utero, cystic lesions that are significant in size may cause fetal hydrops, necessitating antenatal interventions such as the ultrasound-guided thoracocentesis and the placement of thoracoamniotic shunts.…”

Transthoracic catheter drainage for large symptomatic congenital pulmonary airway malformation

“…Congenital pulmonary airway malformation (CPAM) is a rare developmental malformation of the terminal respiratory bronchioles that are replaced by an overgrowth of non‐working cystic tissue . The reported incidence of CPAM ranged from 1 in 25 000 to 1 in 35 000 pregnancies .…”