Congenital Descending Aorta-Pulmonary Vein Fistula

Isolated partial anomalous origin of a branch pulmonary artery from the descending aorta

“…[1][2][3][4] This anomaly is characterised as an anomalous systemic artery arising from the descending aorta supplying the basal segments of the lung which lacks a pulmonary arterial supply, the segments of the lung present a normal bronchial system distribution as well as normal pulmonary parenchyma, and the drainage and return of pulmonary veins are normal. [2][3][4]6 The cause of systemic arterial supply to the normal lung is unknown. 4,5 It was previously classified as Pryce type I sequestration.…”

Surgical management of aorta-pulmonary vein fistulas

“…Among the four cases, there was one case presenting as a fistula between the abdominal aorta and the right inferior pulmonary vein, one case presenting as a fistula between the descending aorta and the right upper pulmonary vein, and two cases presenting as fistulas between the descending aorta and the left inferior pulmonary vein . In one case, the patient was a 7‐day‐old neonate; the patients in the other three cases were adults …”

Congenital Descending Aorta to Pulmonary Vein Fistula

“…Four of the 10 cases were in adults and the rest in children and infants. [1][2][3][4][5][6][7][8][9] Of the 10 reported cases, 6 were in male individuals and 4 were in female individuals. Nearly all of the patients were treated with surgical ligation.…”

“…cDAPVF cDAPVF is characterized by a descending aorta to pulmonary vein fistula with enlarged pulmonary veins, normal pulmonary artery distribution, and no pulmonary parenchymal abnormalities to suggest sequestration. 9 The following cases are used to highlight the relevant anatomy and radiographic findings of cDPAVF.…”

“…Thus, when treating patients with this congenital disorder, surgeons can ligate the descending aortic branch without concern that they will compromise blood flow to that tissue. 8,9 A B C…”