Congenital laryngeal cysts (CLCs) are rare and may be fatal. Although CLCs have the potential to cause severe airway obstruction and death, these are not common presentations at birth. The most common CLCs are the aryepiglottic cysts, with the epiglottic cysts being the least common. In this report, a newborn with severe airway obstruction at birth, caused by a giant congenital epiglottic cyst, is presented.