Congenital Lobar Emphysema in an Adult

Sasieta, Humberto C.; Nichols, Francis C.; Kuzo, Ronald S.; Boland, Jennifer M.; Utz, James P.

doi:10.1164/rccm.201602-0289im

Cited by 7 publications

(9 citation statements)

References 2 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…There have been previously reported cases of patients being diagnosed in adulthood, however these are commonly before the end of the fourth decade of life. [1,2] No previous cases have been reported with this finding or potential causes of worsening. Potential treatments include surgical resection and endobronchial valve replacement.…”

Section: Discussionmentioning

confidence: 79%

Progressive congenital emphysema detected in an elderly adult

Fonseca-Paricio

Khaing

Gupta

et al. 2020

CRIM

View full text Add to dashboard Cite

show abstract

Section: Discussionmentioning

confidence: 79%

Progressive congenital emphysema detected in an elderly adult

Fonseca-Paricio

Khaing

Gupta

et al. 2020

CRIM

View full text Add to dashboard Cite

show abstract

“…CLE is a rare developmental abnormality first described in 1932 and designated in 1951 as pulmonary lobar hyperinflation [1,2], which leads to atelectasis and mediastinal shift secondary to compression of normal tissues by bullous disease. This lung disorder is typically diagnosed during the neonatal period using ultrasound.…”

Section: Commentmentioning

confidence: 99%

“…This lung disorder is typically diagnosed during the neonatal period using ultrasound. Cardinal radiographic features include hyperlucency due to overinflation and air trapping with or without attenuation of pulmonary vasculature within the affected lobe [1,3]. Among the rare congenital lung presentations diagnosed during adulthood, CLE may manifest as recurrent pulmonary infections or respiratory distress but is often asymptomatic.…”

Section: Commentmentioning

confidence: 99%

“…(Ann Thorac Surg 2017;104:e367-9) Ó 2017 by The Society of Thoracic Surgeons C ongenital lobar emphysema (CLE) is a rare lung disorder characterized by lobar hyperinflation and adjacent atelectasis secondary to compression, resulting in respiratory distress. This developmental anomaly is typically diagnosed by 6 months of age and rarely during adulthood [1]. However, inadequate evaluation during the neonatal period and increasing frequency of radiographic imaging has resulted in higher incidence of congenital lung disease among adults.…”

mentioning

confidence: 99%

See 1 more Smart Citation

Near Complete Obliteration of the Left Hemithorax by Congenital Lobar Emphysema in an Adult

King

Ramesh

Essandoh

et al. 2017

The Annals of Thoracic Surgery

View full text Add to dashboard Cite

Congenital lobar emphysema is a rare pulmonary malformation typically diagnosed during infancy and is characterized by bullous disease. A 28-year-old woman, who presented with 1 week of progressive dyspnea and chest pain, was found to have left hemithoracic lung hyperinflation with perfusion deficit upon radiographic evaluation. Bullous disease was found intraoperatively to originate from 1 lower lobe segment. Normal parenchymal lung expansion occurred following resection of the affected segment. Therefore, we present a rare case of congenital lobar emphysema resulting in near-complete occupancy of the left hemithorax and diagnosed in a previously asymptomatic adult without history of predisposing factors.

show abstract

“…Imaging studies are regarded as the gold standard for the diagnosis of CLE, which is characterized by overinflation of the involved lobes [ 1 ]. The most frequently affected lobe is the left upper lobe, followed by the right middle lobe [ 6 , 7 ]. However, multilobar involvement is extremely rare.…”

Section: Introductionmentioning

confidence: 99%

Fatal congenital lobar emphysema in a puerpera: a case report and literature review

et al. 2021

View full text Add to dashboard Cite

Background Congenital lobal emphysema (CLE) is a developmental lung abnormality usually diagnosed in the neonatal period and is rarely observed in adults. Adults with CLE are usually asymptomatic and only a small fraction may present with coughing, recurrent pneumonia and respiratory distress. In imaging studies, the most frequently affected lobe of CLE is the left upper lobe, followed by the right middle lobe. However, multilobar involvement with severe mediastinal shift is extremely rare. Case presentation We report a case of fatal CLE in a 28-year-old puerpera with postpartum respiratory failure. Chest computed tomography (CT) revealed emphysema of the right upper, middle and lower lobes resulting in adjacent atelectasis. Hyperinflation of the right upper lobe crossed the midline, leading to a deviation of the mediastinal structure to the left hemithorax and severe compression of the left lung. Conclusions Early and timely diagnosis of CLE with routine follow-up is necessary for patients. CLE, especially with multilobar involvement or mediastinal shift, could be life-threatening and should be promptly and aggressively treated to prevent severe complications.

show abstract

Congenital Lobar Emphysema in an Adult

Cited by 7 publications

References 2 publications

Progressive congenital emphysema detected in an elderly adult

Progressive congenital emphysema detected in an elderly adult

Near Complete Obliteration of the Left Hemithorax by Congenital Lobar Emphysema in an Adult

Fatal congenital lobar emphysema in a puerpera: a case report and literature review

Contact Info

Product

Resources

About