Congenital Maxillomandibular Fusion: A Rare Case of Isolated True Bony Syngnathia

Abstract

Objective: To present a rare case of congenital maxillomandibular fusion or syngnathia.
 Methods: 
 Study Design: Case report
 Setting: Tertiary Private Teaching Hospital
 Patient: One
 Results: A 3-year-old girl with oral adhesion (syngnathia) caused by a mandibular to maxillary fibrous band underwent successful surgical division of maxillomandibular bony fusion. Subsequent monitoring and serial oral dilations were performed post operatively, resulting in mouth opening of 24mm over a period of 3 months. Currently, the patient is able to tolerate a general liquid diet.
 Conclusion: Congenital maxillomandibular fusion is a very rare condition with few cases reported. We hope this report contributes to its diagnosis and management in other children.
 Keywords: Congenital maxillomandibular fusion, syngnathia