Congenital nasal pyriform aperture stenosis

Pereira, Kevin D.; Wang, Brian S.

doi:10.1016/j.otot.2005.08.002

Cited by 8 publications

(12 citation statements)

References 12 publications

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“…The pyriform aperture is the most anterior and narrow opening of the bony nasal airways. It is limited laterally by the nasal process of the maxilla, inferiorly by the junction of the horizontal process of the maxilla and the anterior nasal spine, and superiorly by the nasal bones [2]. Congenital stenosis of this anatomic region is a rare condition that may present as an isolated malformation or may be associated with other craniofacial anomalies.…”

Section: Introductionmentioning

confidence: 99%

Congenital nasal pyriform aperture stenosis: diagnosis and management

et al. 2012

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BackgroundCongenital nasal pyriform aperture stenosis is a rare and potentially lethal form of airway obstruction in newborns. Immediate recognition and appropriate therapy are mandatory for this potentially life-threating condition. This anomaly may present as an isolated malformation or may be associated with other cranial-facial anomalies. Clinically, CNPS shows unspecific symptoms of nasal airway obstruction such as apnoic crisis, episodic cyanosis and inability to nurse. The purpose of this report is to present author's experience in the surgical management of this rare pathology in 3 patients.Patients and MethodsThree cases of congenital nasal pyriform aperture stenosis were reviewed for presentation of the disorder, management and effectiveness of the surgical treatment.ResultsAll the patients underwent a surgical correction of the pyriform aperture stenosis using a sublabial approach followed by nasal stenting. During the follow-up no cases of restenosis, respiratory failure or cyanosis were detected.ConclusionsCongenital pyriform aperture stenosis should be suspected in newborns with clinical signs of severe nasal obstruction associated with a difficulty to pass a small catheter though the anterior nasal valve. Timely recognition is mandatory to prevent a potential deadly outcome. Surgical correction of the stenosis though a sublabial approach followed by a nasal stenting revealed to be most effective treatment for these patients.

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Section: Introductionmentioning

confidence: 99%

Congenital nasal pyriform aperture stenosis: diagnosis and management

et al. 2012

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“…7,9 Early reports suggested that CNPAS occurred as an isolated anomaly but later studies showed the presence of associated central nervous system, endocrine, or craniofacial abnormalities. 3,8 These anomalies are holoprosencephaly, facial hemangiomas, clinodactyly, pituitary dysfunction, single central maxillar megaincisor, and hypoplastic maxillary sinuses. 3,4,7,8 A central maxillar megaincisor is associated with this disease in 75% of cases.…”

Section: Case Reportmentioning

confidence: 99%

“…3,8 These anomalies are holoprosencephaly, facial hemangiomas, clinodactyly, pituitary dysfunction, single central maxillar megaincisor, and hypoplastic maxillary sinuses. 3,4,7,8 A central maxillar megaincisor is associated with this disease in 75% of cases. 4 In our case, no abnormalities were detected other than CNPAS.…”

Section: Case Reportmentioning

confidence: 99%

“…CNPAS result from the abnormal bony overgrowth of the nasal process of maxilla into the nasal cavity and leads to narrowing of the anterior nasal airway. 1,6,8,10 Stenosis may also result from hypoplastic growth of the primary palate during fetal life. 8 The correct diagnosis of CNPAS is made with CT examination of the nasal cavity by showing the pyriform aperture width is less than 8 mm, 1 such as in our case (5.7 mm).…”

Section: Case Reportmentioning

confidence: 99%

“…1,6,8,10 Stenosis may also result from hypoplastic growth of the primary palate during fetal life. 8 The correct diagnosis of CNPAS is made with CT examination of the nasal cavity by showing the pyriform aperture width is less than 8 mm, 1 such as in our case (5.7 mm). Patients can present at birth with cyanosis, breathing diffi culty, or nasal cavity narrowing to the extent that passage of the nasogastric tube is impossible, or later, with the onset of an upper respiratory infection.…”

Section: Case Reportmentioning

confidence: 99%

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Congenital nasal pyriform aperture stenosis: clinical and radiologic findings and treatment

et al. 2009

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Congenital nasal pyriform aperture stenosis (CNPAS) is an unusual cause of airway obstruction in the newborn and infants. Immediate recognition and therapy are essential for this potentially life-threatening circumstance. CNPAS should be considered in the differential diagnosis of any infant with episodic apnea, cyclical cyanosis, and feeding difficulty. Computerized tomographic (CT) measurements and imaging features enable accurate diagnosis of this abnormality. In this report we demonstrated CT examination findings of CNPAS in a neonate.

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Neonatal Nasal Obstruction

Diop

Balakrishnan

2021

Curr Otorhinolaryngol Rep

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Congenital nasal pyriform aperture stenosis

Cited by 8 publications

References 12 publications

Congenital nasal pyriform aperture stenosis: diagnosis and management

Congenital nasal pyriform aperture stenosis: diagnosis and management

Congenital nasal pyriform aperture stenosis: clinical and radiologic findings and treatment

Neonatal Nasal Obstruction

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