Congenital Pulmonary Airway Malformation – Case Presentation

Abstract

Congenital pulmonary airway malformation (CPAM) is a rare cystic lesion, whose prognosis depends on the extent of the lesion, the association of other congenital abnormalities, the associated pulmonary pathology and the possibility of curative surgery. We present the case of a 5-month-old infant diagnosed with bilateral CPAM, based on clinical and imaging investigations, with acute pulmonary manifestations and without other associated congenital anomalies.

The Evolution of Radiological Images in a 4-Month-Old Infant With Congenital Pulmonary Airway Malformation: A Case Report

“…(2)(3)(4)(5) The location and extent of CPAM should be reported since they are essential for tclinical management and prospective surgical approach. (16) CPAM usually involves one lobe, (4,13,18) with a predilection of the lower lobe. (3,8,9,13,19) CPAM may resemble pneumonia or pulmonary abscess as a result of superimposed infection.…”

“…The prognoses of types 2 and 3 are not as favorable as that of type 1 because of their correlation with other congenital anomalies. (2,18,20) During antenatal imaging, there is a prognostic parameter known as CAM volume ratio (CVR), which compares the volume of the tumor to the fetal head circumference as a standardization of tumor growth relative to gestational age. (6,14,15) Prenatal management of choice includes the administration of steroids to the mother, minimally invasive procedures, or open fetal operation.…”