Congenital pulmonary vascular anomalies

Dimas, Vasiliki V; Dillenbeck, Jeanne; Josephs, Shellie C.

doi:10.21037/cdt.2018.01.02

Cited by 8 publications

(6 citation statements)

References 26 publications

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“…The size of the venous indwelling needle mainly depended on the patient's weight; 24G or 22G venous indwelling needles were most commonly used. The total dosage of the contrast agent was 1.5–2 ml/kg; if this was insufficient, it was diluted with normal saline to maintain a bolus duration of 15–25 s, but the total amount of liquid did not exceed 10 ml/kg ( 11 , 12 ). The scan could be started 1–3 s after the contrast agent was fully injected.…”

Section: Methodsmentioning

confidence: 99%

Proximal interruption of the pulmonary artery: A review of radiological findings

Zhang

Cao²,

Zhou³

et al. 2022

Front. Pediatr.

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ObjectivesProximal interruption of the pulmonary artery (PIPA) has various clinical manifestations. This review focused on and summarized the clinical and radiological features of PIPA, based on relevant literature studies.MethodsThe study included a total of 25 PIPA cases in the Guangzhou Women and Children's Medical Center between January 2015 and December 2021. Conventional chest photographs and chest computed tomography angiography (CCTA) of patients with PIPA were analyzed and summarized.ResultsThe radiological results showed that 17 cases were right-sided and 8 cases were left-sided PIPA. Additionally, the percentage of pulmonary hypoplasia on the affected side was 44%, 36% for pulmonary hypertension, 28% for the mosaic sign, 20% for subpleural cystic lucency shadow, 20% for subpleural serrated shadow, 20% for collateral vessel thickening, 16% for subpleural band-like parenchyma, 12% for pneumonia, and 56% for patent ductus arteriosus.ConclusionThe clinical manifestations of PIPA are non-specific. Awareness of this anomaly, based on radiological manifestations, particularly those observed on CCTA images, is important for ruling out alternative diagnoses and implementing appropriate management.

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Section: Methodsmentioning

confidence: 99%

Proximal interruption of the pulmonary artery: A review of radiological findings

Zhang

Cao²,

Zhou³

et al. 2022

Front. Pediatr.

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“…The incidence of congenital pulmonary artery (PA) anomalies varies widely: that of isolated pulmonary stenosis (PS) is approximately 1/2000 live births while that of pulmonary agenesis is around 1/100 000 live births [1][2][3] . They are part of a heterogeneous spectrum of diseases and their antenatal diagnosis requires good knowledge of fetal cardiac anatomy because their clinical presentation varies depending on the type and severity of the underlying lesion 4 .…”

Section: Introductionmentioning

confidence: 99%

“… Table S1 Typical findings of congenital pulmonary artery anomalies, with illustrated examples of cases 2,3,31–42 (Figures 5–16)…”

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confidence: 99%

Prenatal screening and diagnosis of pulmonary artery anomalies

Lesieur

Zaffran

Chaoui³

et al. 2023

Ultrasound in Obstet & Gyne

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Congenital pulmonary artery anomalies are rare. Their antenatal diagnosis requires good knowledge of fetal cardiac anatomy because their clinical presentation varies depending on the type and severity of the underlying lesion. Screening of these vascular anomalies can be straightforward in some cases because of significant associated consequences that are detected easily on ultrasound, while other anomalies have considerably less obvious features. There may be an associated genetic syndrome. The aim of this review was to define anomalies of the main pulmonary artery and its branches and to propose, through the identification of suspicious findings during routine antenatal heart examination, an optimal screening method for the pulmonary artery pathway. We propose that pulmonary artery anomalies can be classified antenatally into four types of disorder. Herein we describe 14 cases subgrouped accordingly as: anomalies of the pulmonary valvular region, with stenosis or atresia of the valve (n = 4); conotruncal abnormalities (n = 4); anomalies associated with abnormal origin or course of the pulmonary artery (n = 4); and anomalies associated with abnormal growth of the pulmonary artery and its branches (n = 2). We highlight the need to differentiate the three-vessel view from the three-vessel-and-trachea view when assessing a fetus with a congenital pulmonary artery anomaly.

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“…They may be recognized early in infancy while others represented in adulthood. Its age of presentation depends on pulmonary blood flow restriction or plethora [1].…”

Section: Introductionmentioning

confidence: 99%

The Application of Retrospective ECG Gated 320-MSCT Angiography in Diagnosis of Congenital Pulmonary Arterial Anomalies in Pediatrics

Tawheed¹,

Elbadry²,

Elhefnawy³

et al. 2021

IJMI

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Congenital pulmonary arteries anomalies included a wide-ranged spectrum of pathology that is usually associated with other congenital heart diseases. These anomalies can be classified into several major categories, which show considerable overlap among those categories. The aim of this study is to evaluate the role of multi-slice computed tomography (MSCT) angiography in assessment of pulmonary arteries anomalies. This study included 76 patients (42 males and 34 females) with male to female ratio 55.2% to 44.7%. The age of the patients ranged from 4 days to 15 years. The studied cases for pulmonary arteries anomalies were subclassified to anomalies of the caliber, origin and development (conotruncal anomalies). We compared MSCT findings with the data collected by cardiac catheterization and/or operation in 38 patients. 320-MSCT diagnosed cases of pulmonary arterial anomalies with 99% sensitivity, 99.8% specificity, 99% PPV, 99.8% NPV and 93.4% accuracy. This study concluded that MSCT is a non-invasive imaging modality that has a significant value in the evaluation of the congenital pulmonary arteries anomalies and its associated extracardiac anomalies in pediatric patients as well as assessment of post-operative complications. It is superior to ECHO in evaluating the pulmonary artery anomalies specially the pulmonary artery branches which are obscured by aerated lung. Also, there is good outcome of the cases owing to early and accurate diagnosis of the cases and post-operative follow up.

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Congenital pulmonary vascular anomalies

Cited by 8 publications

References 26 publications

Proximal interruption of the pulmonary artery: A review of radiological findings

Proximal interruption of the pulmonary artery: A review of radiological findings

Prenatal screening and diagnosis of pulmonary artery anomalies

The Application of Retrospective ECG Gated 320-MSCT Angiography in Diagnosis of Congenital Pulmonary Arterial Anomalies in Pediatrics

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