Congenital Radio-Ulnar Synostosis

Abstract

Thirty-three patients with congenital radio-ulnar synostosis were examined. There was one familial predisposition. Chromosomal patterns were examined in seventeen patients and were normal. Bone maturation appeared normal. The radial deviation angle, in the patients whose distal radial epiphysis had closed, was elevated (Madelung's deformity). However, in the patients whose distal epiphysis maturation score was 8, it was not elevated. On the other hand, elongation of the ulna (plus variant) and/or dorsal dislocation of the distal end of the ulna was seen in early life. In terms of treatment, all attempts to divide the two bones failed. It was found that derotation of the nonwriting hand by an osteotomy through the proximal fusion mass was a useful procedure.

Treatment of Blocked Elbow Flexion in Congenital Radioulnar Synostosis With Radial Head Excision

“…2,4,10 The deformity results from a failure of longitudinal segmentation. 2,4,10 The deformity results from a failure of longitudinal segmentation.…”

A rare case of congenital humeroradioulnar synostosis from medieval Pawłów Trzebnicki, Poland

“…A review of the palaeopathological and clinical literature illustrates that CULS may also include additional anomalies affecting the upper extremity. The types and severity of malformations vary but may include radial ray defects (e.g., radial hypoplasia to radial aplasia; Madelung's deformity; congenital dislocation of the hip(s); clubfoot; underdeveloped skeletal structures of the forearm; wrist, and/or hand; synostosis of the fibula and tibia; syndactyly; microcephaly; polydactyly; William's syndrome; dwarfism; and oligodactyly, craniosynostosis, and mandibulofacial dysostoses; Mital, ; Schinzel, ; Simmons, Southmayd, & Riseborough, ; Miura, Nakaruma, & Suzuki, ; Cleary & Omer, ; Pagnan, Gollop, & Lederman, ; Hurst, Baraitser, & Wonke, ; Sachar, Akelman, & Ehrlich, ; Waters & Simmons, ; Winfeld & Otero, ). Furthermore, CULS lacks the presence of bone remodelling, sclerotic bone lesions, and the ossification of connective tissues.…”

“…Additionally, radiographs reveal normal skeletal structures (i.e., adjoining epiphyses). However, dwarfism; and oligodactyly, craniosynostosis, and mandibulofacial dysostoses; Mital, 1976;Schinzel, 1980;Simmons, Southmayd, & Riseborough, 1983;Miura, Nakaruma, & Suzuki, 1984;Cleary & Omer, 1985;Pagnan, Gollop, & Lederman, 1988;Hurst, Baraitser, & Wonke, 1991;Sachar, Akelman, & Ehrlich, 1994;Waters & Simmons, 1996;Winfeld & Otero, 2016). Furthermore, CULS lacks the presence of bone remodelling, sclerotic bone lesions, and the ossification of connective tissues.…”

The use of pedicled posterior interosseous fat graft for mobilization of congenital radioulnar synostosis: a case report

“…Derotational osteotomy at the site of synostosis or the diaphysis of the radius and ulna in order to fix the forearm in neutral or mild pronation is currently the accepted treatment for synostosis. 2,8,11 Most efforts to separate the synostosis and obtain rotation of the forearm have ended in failure. Yabe 12 released the synostosis and interposed the anconeus muscle to preserve the separation of the radius and ulna.…”

“…Yabe 12 released the synostosis and interposed the anconeus muscle to preserve the separation of the radius and ulna. Miura et al 8 performed Yabe's procedure and reported that all 8 cases resulted in recurrence of the synostosis. Ikegami et al 4 reported that 5 of 7 cases achieved forearm rotation after Yabe's procedure.…”