Congenital salivary fistula of an accessory parotid gland in Goldenhar syndrome

Abstract

A congenital cheek salivary fistula of an accessory parotid gland should be considered indicative of Goldenhar syndrome.

Cheek fistula from the ectopic salivary gland: A variant of the oculo‐auriculo‐vertebral spectrum

“…According to previous reports and the present study, CCSF occurs with a very distinct set of malformations, and the following common features should be noted: 1) congenital cheek saliva‐discharging orifice lateral to the oral commissure; 2) presence of ectopic salivary gland connected to the skin orifice through a fistulous tract; 3) the fistulous tract does not communicate with Stensen's duct; 4) the ectopic salivary gland is located in the buccal space anterior to the masseter, inferior to Stensen's duct, and superficial to the buccinators; 5) Stensen's duct can be normal and intact; 6) the presence of ipsilateral preauricular appendage; and 7) ipsilateral hypoplasia of the mandible. Coexistence of the cheek saliva‐discharging fistula and preauricular appendage is a prominent clinical feature of this syndrome.…”

“…An ipsilateral preauricular appendage is another frequent diagnostic sign. In our previous study, we have additionally reported that moderate mandibular hypoplasia constitutes another clinical feature …”

“…CCSF is very rare, and there are only 10 documented cases in the English literature . We have previously reported three cases in two articles .…”

“…The development of a congenital cheek salivary fistula (CCSF) from ectopic accessory gland tissue has been documented as a very rare clinical entity. [1][2][3] It is characterized by the occurrence of a saliva-discharging skin fistula lateral to the oral commissure. [2][3][4][5][6][7][8][9] An ipsilateral preauricular appendage is another frequent diagnostic sign.…”

“…[1][2][3] It is characterized by the occurrence of a saliva-discharging skin fistula lateral to the oral commissure. [2][3][4][5][6][7][8][9] An ipsilateral preauricular appendage is another frequent diagnostic sign. In our previous study, we have additionally reported that moderate mandibular hypoplasia constitutes another clinical feature.…”