Congenital Spinal Extradural Cyst in Two Siblings

Chynn, K.-Y.

doi:10.2214/ajr.101.1.204

Cited by 56 publications

(29 citation statements)

References 23 publications

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“…The dural sleeve of the nerve root or the junction of the sleeve and thecal sac are the most common sites for these defects, although less commonly the dorsal midline of the thecal sac is involved. [1][2][3][4] The theory of a congenital origin is further supported by reports of a familial syndrome comprising multiple spinal arachnoid cysts, lower-extremity lymphedema (Milroy disease), and distichiasis (double rows of eyelashes).…”

Section: Mechanisms Of Pathogenesismentioning

confidence: 99%

Spinal extradural arachnoid cysts: clinical, radiological, and surgical features

Liu

Cole

Kan

et al. 2007

FOC

106

154

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✓Extradural arachnoid cysts in the spine are rare and are seldom a cause of spinal cord compression. They are thought to arise from congenital defects in the dura mater, and they almost always communicate with the intrathecal subarachnoid space through a small defect in the dura. The mainstay of treatment in patients with neurological symptoms is surgical removal of the cyst together with ligation of the communicating pedicle and closure of the dural defect. In the present paper the authors review the literature and discuss the clinical and pathological features, mechanisms of pathogenesis, neuroimaging characteristics, and surgical management of spinal extradural arachnoid cysts. The surgical technique for removal of these lesions is illustrated in a patient with a large thoracolumbar spinal extradural arachnoid cyst causing neurogenic claudication.

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Section: Mechanisms Of Pathogenesismentioning

confidence: 99%

Spinal extradural arachnoid cysts: clinical, radiological, and surgical features

Liu

Cole

Kan

et al. 2007

FOC

106

154

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“…23,[31][32][33] This is also supported in their association with congenital neural tube defects such as spina bifida occulta and diastematomyelia. 34,35 Moreover, the presence of these cysts as a part of a hereditary syndrome caused by an autosomal dominant disorder with variable expression including distichiasis or double eyelashes, lymphedema, congenital heart disease and cleft palate point to its genetic etiology.…”

Section: A 1dmentioning

confidence: 87%

Spinal extradural arachnoid cysts

et al. 2013

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Objective: Extradural arachnoid cysts (EACs) are rare causes of spinal cord compression and cauda equina. These benign lesions appear in the literature mainly as single case reports. In this article, we present the largest series found in literature, with four new cases of spinal extradural arachnoid cysts. The characteristic imaging features, details of surgical steps and strategies to prevent postoperative kyphosis in this cystic pathology will be discussed.

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“…Hereditary recurrent cholestasis with lymphedema (Aagenaes, 1974) is an autosomal recessive condition, but it is characterized by neonatal intrahepatic cholestasis with jaundice. Congenital lymphedema with distichiasis and progressive weakness of the legs due to a spinal extradural cyst is also an autosomal recessive condition (Chynn, 1967). …”

Section: Discussionmentioning

confidence: 99%