Congenital urethrovaginal fistula with transverse vaginal septum

Abstract

Congenital urethrovaginal fistula is an extremely rare genitourinary anomaly. Literature search identified only five reported cases, all of which were associated with urogenital abnormalities. Transverse vaginal septum is another rare condition, resulting from abnormalities in the vertical fusion between the vaginal components of the Mullerian ducts and the urogenital sinus; and associated fistulous connection of the vagina with the urethra is even rarer. Herein we describe the case of a 35-year-old woman who presented with dyspareunia, and a 1-year history of infertility, who was found to have a urethrovaginal fistula with low transverse vaginal septum. The patient was successfully treated with excision of the septum and closure of the urethrovaginal fistula.

A rare case of persistent urogenital sinus in an adult woman associated with unilateral rudimentary horn with ipsilateral renal agenesis and contralateral dermoid cyst

“…Here in the current case, I describe a very rare congenital anomaly in an adult female which initially made a great difficulty in its identification whether it is PUGS or low transverse vaginal septum with low urethrovaginal fistula [11]. In the later, the septum ought to be restricted distinctly to the vaginal hole, however here the septum stretches out anteriorly to underneath the level of the external urethral meatus covering all the vestibular area making a free communication between the urinary and genital system over the septum that structure the floor of the sinus, with a solitary vulval opening channels both menstrual blood and urine.…”

A Case of Congenital Urethrovaginal Fistula in a Female Child with Suspected Imperforate Hymen: A Case Report

“…This is often iatrogenic from postsurgical procedure, obstetric complication, pelvic trauma, neoplasm and pelvic irradiation [1,4]. In children congenital anomaly may also be the cause1.congenital Urethrovaginal fistula is an extremely rare genitourinary anomaly [5,6]. The reported five cases in the literature are all associated with urogenital abnormalities like vaginal septum, vaginal agenesis and imperforate hymen [5,6,7].…”

“…The mainstay of treatment is surgical, this comprise of excision of the transverse vaginal septum and closure of the urethrovaginal fistula [5,6].…”

Robotic management of congenital urethra-vaginal fistula with transverse vaginal septum

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_______________________________________________________________________________________ Introduction:The transverse vaginal septum (TVS) with congenital urethra-vaginal fistula (CUVF) is a rare anomaly of the mullerian duct (1, 2). Incomplete channelling of the vaginal plate, or an abnormality in the fusion of the vaginal component of mullerian duct with the urogenital sinus results in TVS (1,3,4). High CUVF occurs due to the persistent communication between the urogenital sinus and utero-vaginal primordium at the tubercle sinus, whereas low CUVF is due to excessive apoptosis of the vaginal plate during channelling (5).

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