HistoryA 50-year-old man was referred for management of a long-standing, large-angle exotropia and limitation of adduction in the left eye. He had a history of poor vision in the left eye since childhood and 4 previous strabismus procedures. The most recent strabismus surgery was 38 years before presentation. Prior records were unavailable, and the patient could not recall any details pertaining to his earlier procedures or alignment in childhood. His wife did not report any recent change in his appearance or alignment.
ExaminationBest-corrected visual acuity was 20/15 in the right eye and 20/200 in the left eye. There was no afferent pupillary defect, and color vision was full and symmetric. The patient had an exotropia of 40 prism diopters (PD) at distance and 45 PD at near, with a −3 adduction deficit of the left eye greatly increasing the exotropia in right gaze to 60 PD. There was a 2 mm ptosis of the left upper eyelid.Anterior segment examination revealed conjunctival scarring over the medial and lateral fornices of both eyes. A palpable, painless, soft, purple-gray mass, 8 mm in horizontal diameter and of indeterminate depth was detected in the superonasal aspect of the orbit of the left eye. It extended subconjunctivally posterior to the caruncle and superonasally toward the upper lid. One large superficial conjunctival vessel penetrated the lesion (Figure 1). The bulk of the mass was apparent through closed lids. The patient was unaware of the presence of this mass. The remainder of the ophthalmological examination was unremarkable, including anterior chamber evaluation, intraocular pressure, fundus examination, and visual fields.
Ancillary TestingDue to the heterogeneous color of the mass, the penetrating vessel, and the lack of adequate history, magnetic resonance imaging (MRI) of the orbits was performed to rule-out malignancy. The MRI showed a well-encapsulated cyst overlying the medial globe, with no evidence of erosion or invasion of surrounding structures. The medial rectus muscle appeared to insert at the posterior pole of the cyst (Figure 2).