Cor Triatriatum: A Review

Abstract

Cor triatriatum is a rare congenital cardiac anomaly, characterized by a fibromuscular partition dividing the left (cor triatriatum sinister) or, rarely, the right atrium (cor triatriatum dexter). Occurring in 0.1–0.4% of congenital heart disease cases, it exhibits diverse clinical presentations, often mimicking mitral stenosis and left-sided heart failure, while occasionally remaining asymptomatic into adulthood. The embryological origin of cor triatriatum remains controversial. Recent years have seen the emergence of new classification systems that offer enhanced prognostic insights. Transthoracic echocardiography is the diagnostic cornerstone. Surgical resection, preferably under cardiopulmonary bypass, is the mainstay treatment, and is associated with favorable long-term outcomes.

Exploring new frontiers: a rare case of catheter ablation for persistent atrial fibrillation in a patient with cor triatriatum sinister guided by intracardiac echocardiography

“…Cor triatriatum is an uncommon congenital cardiac anomaly, comprising 0.1-0.4% of congenital heart diseases. This condition is identified by the unique feature of the left or right atrium being split into two separate chambers due to the presence of an abnormal fibromuscular membrane [1,2]. The more common left-sided variant, CTS often coexists with other congenital heart defects such as atrial septal defects, patent foramen ovale, or left-sided superior vena cava [2].…”