Cor triatriatum dexter associated with atrial septal defect: Management in a complex clinical case

Sozzi, Fabiola B.; Montanaro, Claudia; Bacà, Laura; Viani, Giacomo Maria; Zilocchi, Massimo; Canetta, Ciro; Meazza, Roberto; Pavone, Laura; Lombardi, Federico

doi:10.1111/echo.13714

Cited by 3 publications

(7 citation statements)

References 5 publications

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“…Those individuals with the division of the morphologically right atrium were diagnosed between the ages of 1 day and 86 years, with a median of 23 years 23–28,31,32,34–91 . Among these individuals, seven‐tenths were female.…”

Section: Resultsmentioning

confidence: 99%

“…They depend on the degree of the partitioning of the right atrium, the patency of the atrial septum, and the extent of any obstruction to flow. In the absence of interatrial communication, and with no obstruction to flow, patients may remain asymptomatic, with the lesion discovered as a chance finding 23–28,31,32,34–88 . When the atrial septum is patent, individuals may present with varying degrees of intermittent cyanosis, syncope, paradoxical systemic, and coronary embolism ranging from severe hypoxia after birth to cyanosis in childhood 23–25,27,32,38–50 .…”

Section: Discussionmentioning

confidence: 99%

“…In the absence of interatrial communication, and with no obstruction to flow, patients may remain asymptomatic, with the lesion discovered as a chance finding 23–28,31,32,34–88 . When the atrial septum is patent, individuals may present with varying degrees of intermittent cyanosis, syncope, paradoxical systemic, and coronary embolism ranging from severe hypoxia after birth to cyanosis in childhood 23–25,27,32,38–50 . The differential diagnosis includes a flail tricuspid valvar leaflet, a small right heart thrombus, or a pedunculated right atrial myxoma.…”

Section: Discussionmentioning

confidence: 99%

“…On this basis, it proved possible to make an individualized review of 193 investigations 1–193 . These findings were then incorporated, as far as possible, with the results of a systematic review of ...…”

Section: Methodsmentioning

confidence: 99%

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Surgical management of divided atrial chambers

Sankhyan

Anderson

Chowdhury

et al. 2021

Journal of Cardiac Surgery

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Background and Aim The morphological variations when one, or both, of the atrial chambers is subdivided, are many and varied. We sought to address clinical presentations, potentially misdiagnosed cases, diagnostic modalities, surgical approaches, and outcomes of this “family” of uncommon lesions. Methods A total of 193 published investigations were synthesized. Diagnostic information was provided by clinical presentation, and multimodality imaging studies. Results Almost three‐quarters of patients with divided atrial chambers present during infancy with severe pulmonary hypertension and cardiac failure. Associated cardiac and extra‐cardiac defects are present in between half and nine‐tenths of cases. Acquired division of the left atrium has been reported after the Fontan operation, orthotopic cardiac transplantation, and complicated aortic valvar infective endocarditis. Surgery under cardiopulmonary bypass remains the definitive treatment. Balloon dilation may be considered in anatomically compatible variants in the setting of cardiac failure and pregnancy as a bridge todefinitive treatment. Overall, mortality has been cited between nil to 29%. Presentation during infancy, associated congenital anomalies, pulmonary hypertension, and surgery in the previous era, have been the reported causes of death. The operative survivors have long‐term favourable outcomes, with near normal cardiac dimensions and low risk of recurrence. While asymptomatic patients with division of the right atrium do not need treatment, surgical resection of the dividing partition under cardiopulmonary bypass is recommended in symptomatic patients with complex anatomy, the spinnaker malformation, or associated cardiac anomalies. Balloon dilation may be considered in uncomplicated patients with less obstructive lesions. Hybrid intervention and endoscopic robotic correction also have been performed. Conclusions Resection of the dividing shelf allows the survivors to regain near normal dimensions with a low risk of recurrence. We submit that an increased appreciation of the anatomic background to division of the atrial chambers will contribute to improved surgical management.

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Section: Resultsmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Methodsmentioning

confidence: 99%

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Surgical management of divided atrial chambers

Sankhyan

Anderson

Chowdhury

et al. 2021

Journal of Cardiac Surgery

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show abstract

“…Our patient is a potential candidate for percutaneous PFO closure. Nevertheless, the presence of CTD is expected to render any percutaneous intervention that involves manipulation of catheters and devices into the right atrium very challenging (ie, difficult catheter navigation or entrapment of the sheaths and/or the closure device) …”

mentioning

confidence: 99%