Cor triatriatum dexter: unusual features in utero and after birth

Fesslová, Vlasta; Saracino, Antonio; Nuri, Halkawt; Pomè, Giuseppe

doi:10.1093/icvts/ivr096

Cited by 7 publications

(4 citation statements)

References 9 publications

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“…The prenatal diagnosis of PRVV primarily relies on echocardiography, which may reveal an undulating echogenic mass or membranous strands in the RA, typically visible after 19 w.g. ( 4 , 5 , 7 , 8 , 10 , 11 ). During diastole, PRVV can obstruct RV inflow by protruding into the TV or RV, causing various non-specific indirect signs.…”

Section: Discussionmentioning

confidence: 99%

“…Even if valve remnants remain, the prognosis can be similar to that of regressed remnants and may be favorable with follow-up ultrasonography. Valve remnants were observed in several cases in the review, except for one case with EV or CN in which surgery was performed after birth ( 10 ). However, further developments remain unknown in fetuses diagnosed at an early stage of pregnancy with an impaired fetal condition from other causes.…”

Section: Discussionmentioning

confidence: 99%

See 1 more Smart Citation

Persistent right venous valve as a cause of fetal and neonatal pathology from prenatal to postnatal periods: a case report and review

Liu,

Wu,

Wang

et al. 2023

Cardiovasc Diagn Ther

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Background Neonatal cyanosis is a clinical manifestation of hypoxemia and is usually pathological. Persistent right venous valve (PRVV) is a rare cause of cyanosis in newborns and can cause prenatal abnormalities, the clinical significance of which varies depending on the severity of the abnormality. There have been few reports on the intrauterine detection of these abnormalities and their follow-up during infancy. Here, we report a case of PRVV causing supravalvular tricuspid valve (TV) obstruction and secondary right ventricle (RV) hypoplasia. This case is unique in terms of its early prenatal detection, distinct cardiac anomalies, and successful surgery that reversed the symptoms, and the findings offer insights into the diagnosis and management of such rare cardiac conditions. Case Description We report a case of a newborn diagnosed with PRVV at 31 weeks of gestation at our center. There was no underlying family history of congenital heart disease. Prenatal sonography identified an echogenic membrane in the right atrium, suggesting TV obstruction and subsequent RV hypoplasia. After birth, the neonate suffered hypoxia with decreased arterial oxygen saturation (SaO 2 ). Minimally invasive surgery successfully corrected the membrane. Postoperative SaO 2 improved immediately. Three months later, follow-up echocardiography revealed normalized TV and RV dimensions. The patient demonstrated steady progress without any complications. We also reviewed previous cases of PRVV before and after birth and summarized the sonographic and clinically relevant features. Conclusions Although PRVV is typically considered as a benign structure, it may lead to significant clinical complications, particularly in fetuses and neonates. The precise identification of its variant forms and related flow patterns is crucial to inform decisions regarding patient management.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Persistent right venous valve as a cause of fetal and neonatal pathology from prenatal to postnatal periods: a case report and review

Liu,

Wu,

Wang

et al. 2023

Cardiovasc Diagn Ther

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“…This newborn underwent surgery during postnatal period due to desaturation of 75% to 85%. [5] Mackman et al published series of 3 cases with neonatal cyanosis. Most patients have either slightly decreased peripheral oxygen saturation or they are completely asymptomatic.…”

Section: Discussionmentioning

confidence: 99%

A Rare Case: Cor Triatriatum Dexter

Orgun¹

2017

South Clin Ist Euras

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Cor triatriatum dexter (CTD) is a rare congenital heart disorder that is result of persistence of the right valve of the embryonic sinus venosus. Clinical significance of CTD is related to degree of obstruction. Asymptomatic patients may be diagnosed during echocardiographic examination performed for unrelated reasons. Presently described is case of a 12-year-old girl with initial diagnosis of acute rheumatic fever whose echocardiogram revealed presence of CTD. Aim of this report was to emphasize that diagnosis of CTD can be difficult and requires careful evaluation of the right atrium by echocardiogram.

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“…Cor triatriatum is one of the rare forms of acyanotic congenital heart disease (ACHD) with an estimated reported incidence rate of 0.1% of all congenital cardiac anomalies [1]. The left atrial form is known as cor triatriatum sinistrum (CTS) and the right atrial form is known as cor triatriatum dexter (CTD).…”

Section: Introductionmentioning

confidence: 99%

Pseudo-cor triatriatum dexter: Rare and asymptomatic but clinical consequences are contemplative

Keyur¹,

Vanani²

2021

Int J Case Rep Images

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Introduction: Congenital anatomic variants are more frequent in the right atrium. Complete or incomplete bisection of the right atrium by a membrane-like fold across the cavity is designated as cor triatriatum dexter. Even though most of the cases of congenital atrial remnants are asymptomatic, the clinical consequences in the presence of cardiovascular diseases are very contemplative.Case Report: We report a case of an elderly patient with acute coronary syndrome and an incidental finding of pseudo-cor triatriatum dexter. Coronary angiography and intervention was done without any complications. Conclusion:Being an extremely rare entity, a partial form of cor triatriatum dexter is an important congenital anomaly to document on echocardiography, and clinical implications could be correlated by clinicians during the management of multidisciplinary diseases.

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Cor triatriatum dexter: unusual features in utero and after birth

Cited by 7 publications

References 9 publications

Persistent right venous valve as a cause of fetal and neonatal pathology from prenatal to postnatal periods: a case report and review

Persistent right venous valve as a cause of fetal and neonatal pathology from prenatal to postnatal periods: a case report and review

A Rare Case: Cor Triatriatum Dexter

Pseudo-cor triatriatum dexter: Rare and asymptomatic but clinical consequences are contemplative

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