Brain echinococcosis is the most common brain parasitic infection in the world. It happens in a very rare location, representing 1% to 2% all cases with hydatid disease. It is more common by approximately 50-70% in pediatric population and young adultswith a male predominance. The definite hosts of echinococcus are various carnivores; man is an accidental host. The growth of hydatid cysts is usually slow and asymptomatic, and clinical manifestations are caused by compression of the involved organ. CT provides definitive results of diagnosis. It shows hydatid cyst as a spherical, well defined, thin walled, homogeneous and non-enhancing cystic lesion without peripheral oedema. Dowling technic is the most commonly done procedure designed to give birth to the intact cyst by irrigating saline between cyst wall-brain interfaces. Medical treatment can be indicated in multiple locations and in cases with peroperative rupture. Prognosis is often good, but same complications can occur after surgery and depend on the location, the size, the number of cysts and the technique used.