Craniofacial fibrous dysplasia

Jhamb, Aakarsh; Mohanty, Sujata; Jhamb, Parul A

doi:10.4103/0973-029x.102523

Cited by 4 publications

(11 citation statements)

References 18 publications

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“…Some authors however do not classify the craniofacial FD into monostotic or polyostotic form at all. They just regard the FD as CFD per se [ 48 - 54 ]. According to them, CFD is not truly monostotic because of the involvement of multiple adjacent bones of the craniofacial skeleton [ 22 , 24 , 48 , 49 , 54 ].…”

Section: Discussionmentioning

confidence: 99%

“…They just regard the FD as CFD per se [ 48 - 54 ]. According to them, CFD is not truly monostotic because of the involvement of multiple adjacent bones of the craniofacial skeleton [ 22 , 24 , 48 , 49 , 54 ]. Similarly CFD is not even polystotic because in some cases bones outside the craniofacial complex are usually not involved [ 22 , 24 , 48 , 49 , 54 ].…”

Section: Discussionmentioning

confidence: 99%

“…The affected part may lose its anatomical shape and become spherical, thus may appear more cosmetically deformed. Sarcomatous transformation however should always be ruled out in such clinical presentations [ 47 , 54 - 59 ].…”

Section: Discussionmentioning

confidence: 99%

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Computed Tomography in Craniofacial Fibrous Dysplasia: A Case Series with Review of Literature and Classification Update

Gupta¹,

Garg²,

Mittal³

2017

TODENTJ

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Introduction:Fibrous dysplasia (FD) is a fibroosseous lesion of the osseous structures of the body. It is not a commonly reported lesion yet it is considered as an important lesion which can affect the maxillofacial region as well. As a result, it can cause deformity of the jaw bones which can further lead to severe facial asymmetry. Craniofacial fibrous dysplasia (CFD) is one of the subtypes of FD that can affect the bones of the craniofacial complex, including the mandible and maxilla. It can also present as facial asymmetry and can be investigated with the help of Maxillofacial Radiology and Imaging. The radiographic findings may vary according to the extent and degree of the disease. Although conventional radiographs provide a good clue regarding the lesion, advanced maxillofacial imaging is capable of providing detailed extent of the disease. Furthermore the classification of CFD is not very clear in the literature. Case Report:This particular paper attempts to document and report the CT appearance of CFD with an attempt to propose a better classification system for the same. Four different patients are reported which presented with FD with involvement of bones of craniofacial region. Working diagnosis of CFD was made with the help of clinical features as well as with radiographic assessment. Advanced imaging included CT scan of the lesions. The article highlights the importance of computed tomography in diagnosis as well as assessment of extent of the disease. Conclusion:It can be concluded that the Dental professionals must be aware regarding the different radiographic appearances of CFD. Advanced imaging modality like CT can provide with exact diagnosis as well as extent of the lesions like FD. Further collaboration of researchers is required to incorporate this proposed change in classification of CFD.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

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Computed Tomography in Craniofacial Fibrous Dysplasia: A Case Series with Review of Literature and Classification Update

Gupta¹,

Garg²,

Mittal³

2017

TODENTJ

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“…Bu Ģekilde tutulumun gözlemlendiği kemikler arasında; maksilla, sfenoid, temporal, frontal, oksipital, parietal kemikler sayılabilir. 2,16 Bu nedenle maksillada görülen vakalar orta suturu geçerek karĢı maksillada da tutulum gösterebilir. 2 FD, femurun proximalini tutarak "shepherd's crook" olarak anılan deformiteyi meydana getirir.…”

Section: Gġrġġunclassified

“…16 Bundan dolayı PFD"nin konjenital olduğu düĢünülmektedir. 16 MAS, PFD ile beraber deride sütlü kahve lekeleri, erken puberte, hipertiroidi, hipofiz adenomu, Cushing sendromu gibi endokrin anomalilerin görüldüğü sendromdur. 21 PFD hastalarının % 3"ünün MAS"a sahip olduğu bildirilmiĢtir.…”

Section: Gġrġġunclassified

Fi̇bröz Di̇splazi̇: Derleme

Naralan¹,

Çağlayan²,

Cantürk³

et al. 2020

Atatürk Üniversitesi Diş Hekimliği Fakültesi Dergisi

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Fibröz displazi (FD), normal kemik dokusunun fibröz dokuyla yer değiĢtirmesi sonucu oluĢan fibro-osseoz bir lezyondur. Vücutta kraniyofasiyal kemiklerde olabileceği gibi diğer kemiklerde de görülebilir. FD, tek bir kemikte tutulum gösteriyorsa monostotik fibröz displazi (MFD), birden fazla kemikte tutulum gösteriyorsa poliostotik fibröz displazi (PFD) adını almaktadır. Ayrıca genel sistemik etkileri olan McCune-Albright sendromunun (MAS) bir komponenti olarak da görülebilmektedir. Tedavisinde, takipten cerrahi rezeksiyona kadar birçok yol izlenebilmektedir. Bu makalede FD"nin etiyolojisi, klinik davranıĢları, histopatolojisi, radyolojik özellikleri, ayırıcı tanısı ve tedavisi hakkında detaylı bilgi verilmiĢtir. Anahtar kelimeler: Fibröz displazi, McCune-Albright Sendromu, Monostotik fibröz displazi, Poliostotik fibröz displazi ABSTRACT Fibrous dysplasia (FD) is a fibro-osseous lesion caused by the replacement of normal bone tissue with fibrous tissue. It can be seen in craniofacial bones in the body or in other bones. If FD shows involvement in a single bone, monostotic fibrous dysplasia (MFD) is referred to as polyostotic fibrous dysplasia (PFD), if it shows involvement in more than one bone. It can also be seen as a component of McCune-Albright syndrome (MAS) with general systemic effects. In the treatment, many paths can be followed up from follow-up to surgical resection. In this article, detailed information about etiology, clinical behavior, histopathology, radiological features, differential diagnosis and treatment of FD are given.

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Maxillofacial fibrous dysplasia—diagnosis, treatment and reconstruction with a personalized, 3D-printed titanium implant: a case report

Dudzińska-Filkiewicz

Łączkowska-Serafin

Krysztopik

et al. 2022

Preprint

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Fibrous dysplasia is a rare disease belonging to benign, noncancerous bone and fibrous-related developmental disorders. A 34-year-old male was admitted to the maxillofacial surgery unit to diagnose a rapidly growing, painless lesion with swelling in the right buccal region and increasing facial deformity for three months. Computed tomography (CT) images revealed an inhomogeneous, ill-defined lesion in the maxilla and maxillary sinus. Despite the lesion, the patient had no clinically significant neurological abnormalities. The lesion was diagnosed as fibrous dysplasia on the basis of preoperative tissue biopsy. The treatment of choice was complete surgical excision with immediate reconstruction and fixation of the orbital floor by implanting an alloplastic titanium mesh implant. Then, the patient underwent a secondary reconstruction of tissue defects using a personalized, 3D-printed titanium implant. Reconstruction of postresection defects covering a large craniofacial area is a challenge for maxillofacial surgeons due to the specific location of the face, especially considering psychological and technical aspects. The reconstruction method should be predictable and safe and should guarantee the best aesthetic effect, close to perfection. The ideal solution seems to be the use of an individually prepared, personalized 3D-printed titanium implant with anatomical detail mapping, which can perfectly recreate the missing tissues.

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Craniofacial fibrous dysplasia

Cited by 4 publications

References 18 publications

Computed Tomography in Craniofacial Fibrous Dysplasia: A Case Series with Review of Literature and Classification Update

Computed Tomography in Craniofacial Fibrous Dysplasia: A Case Series with Review of Literature and Classification Update

Fi̇bröz Di̇splazi̇: Derleme

Maxillofacial fibrous dysplasia—diagnosis, treatment and reconstruction with a personalized, 3D-printed titanium implant: a case report

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