Cryptogenic bilateral fibrosing pleuritis

Immunosuppressant-Responsive Idiopathic Lymphocytic Pleuritis

“…Familial cryptogenic fibrosing pleuritis that is unresponsive to corticosteroids has been described in association with Fanconi’s syndrome [9]. Buchanan et al [10]describe four cases of cryptogenic bilateral fibrosing pleuritis with similar features to our cases. Focal collections of lymphocytes were present in the cases described.…”

Restrictive allograft syndrome post lung transplantation is characterized by pleuroparenchymal fibroelastosis

“…It is characterized radiologically by features suggestive of a chronic interstitial pneumonia with upper lobe predominance, and histologically by pleural fibrosis and parenchymal fibroelastosis in a predominantly subpleural distribution, with a sharp demarcation between fibroelastotic and unaffected lung parenchyma, and with the presence of fibroblastic foci at this interface. A limited number of cases with similar radiologic and pathologic features have also been reported, [8][9][10][11][12][13][14] including a very recent article by Reddy et al, 14 suggesting a broader spectrum of histopathologic findings.…”

“…Several cases and small series with similar radiologic and pathologic features have also been reported. [8][9][10][11][12][13][14] Radiologically, idiopathic pleuroparenchymal fibroelastosis has been characterized by pleural thickening associated with underlying parenchymal reticular abnormalities, architectural distortion and traction bronchiectasis in a mostly upper lobepredominant distribution. 7,10,11 Histologically, idiopathic pleuroparenchymal fibroelastosis is characterized by pronounced visceral pleural fibrosis associated with subpleural, 'intra-alveolar' fibrotic changes characterized by an admixture of elastic and fibrous tissue (fibroelastosis).…”

Syndrome of pleural and retrosternal "bridging" fibrosis and retroperitoneal fibrosis in patients with asbestos exposure

“…Pleural fibrosis is most commonly caused by asbestos exposure and may follow asbestos-related benign pleural effusion,1 tuberculous pleural effusion, haemothorax, use of ergot derivatives, and occasionally rheumatoid pleurisy, uremic pleuritis or coronary artery bypass graft surgery; rarely it may remain idiopathic,1 , 2 occasionally in a familial context 3 , 4. Mediastinal fibrosis may develop as a consequence of histoplasmosis or tuberculosis, or rarely actinomycosis, syphilis, aspergillosis, sarcoidosis, silicosis or methysergide exposure, or it may remain idiopathic 5.…”