Cystic adenomatoid malformation of the lung: A diagnostic dilemma

Mohta, Anup; Kanojia, Ravi Prakash; Bathla, Sapna; Khurana, Nita

doi:10.4103/0189-6725.54776

Cited by 6 publications

(5 citation statements)

References 7 publications

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“…CCAM represents focal pulmonary dysplasia as confirmed by identification of skeletal muscle within cyst wall. [4] Embryologically, based on anatomical changes occurring in lung, vertebrate lung development has been subdivided into five distinct periods: embryonic (3-7 weeks), pseudoglandular (7-17 weeks), canalicular (17-29 weeks), saccular (24-36 weeks), and alveolar (36 weeks to maturity). The CCAM develops during pseudoglandular and saccular period (7-35weeks).…”

Section: Discussionmentioning

confidence: 99%

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Type I Congenital Cystic Adenoid Malformation Causing Right Mediastinal Shift in a Two Years Old Child

Kamble¹,

Thawait²,

Kamble³

2014

jemds

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Congenital cystic adenomatoid malformations (CCAM) of lung are rare, congenital, cystic, developmental hamartomatous malformation of lung, arising from excessive disorganized proliferation of tubular bronchial structures. Very few cases have been reported in literature. Although it is a disorder of infancy, majority of cases are being diagnosed within first two years of life. We describe CCAM in two years old girl who presented with recurrent lower respiratory tract infections, since infancy and had type I CCAM of upper and middle lobe causing mediastinal shift to right.

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Section: Discussionmentioning

confidence: 99%

“…The CCAM develops during pseudoglandular and saccular period (7-35weeks). [4] The incidence of CCAM is one in 25,000 to 1 in 35,000 pregnancies with males and females equally affected. CCAM constitutes 25% of all congenital lung lesions.…”

Section: Discussionmentioning

confidence: 99%

Type I Congenital Cystic Adenoid Malformation Causing Right Mediastinal Shift in a Two Years Old Child

Kamble¹,

Thawait²,

Kamble³

2014

jemds

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“…These are believed to represent focal pulmonary dysplasia because skeletal muscle may be identified from within the cyst wall. 4 Male subjects are affected as frequently as female subjects. The left lung is involved as often as the right lung with single lobe disease observed four times more often than multilobe disease.…”

Section: Case Reportmentioning

confidence: 99%

Congenital Cystic Adenomatoid Malformation in an Adolescent: An Unusual Presentation with Pleural Effusion and Pneumatocele

Anand¹,

Deshmukh²,

Naik³

et al. 2022

The Indian Journal of Chest Diseases and Allied Sciences

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Congenital cystic adenomatoid malformation (CCAM) encompasses a continuum of hamartomatous cystic lung lesions characterised by the presence of abnormal bronchiolar structures of varying sizes or distribution. The CCAM is a disorder of infancy with majority of the cases being diagnosed within the first two years of life. We describe CCAM in a 13-yearold girl complaining of recurrent lower respiratory tract infections since infancy who presented with post-infectious pneumatocele with loculated pleural effusion, and suspected abscess formation and had undergone resection.

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“…3 It arises from excessive disorganized proliferation of tubular bronchial structures excluding the alveoli which are believed to represent focal pulmonary dysplasia. 4 In this anomaly, an entire lobe of the lung is replaced by a non-working cystic mass of abnormal lung tissue whose blood supply is derived from the normal lung circulation. 5 Although the cause is unknown, 1 they are considered to be bronchopulmonary foregut malformations, probably caused by an arrest in lung development between the fourth and seventh week of fetal life.…”

Section: Introductionmentioning

confidence: 99%