Cystic lymphangioma of the adrenal gland: report of a case and review of the literature

Abstract

BackgroundCystic lymphangioma is a rare tumor of the lymphatic vessels that occurs more frequently in women. Location of this pathology can be diverse but most commonly occurs in the neck or axilla. Cystic lymphangioma originating from the adrenal tissue represents a very rare entity.Case presentationWe report here the case of a 38-year-old woman who was diagnosed with a cystic retroperitoneal mass. After further investigations, the patient was suspected to have a left adrenal cystic lymphangioma. She underwent successful open left adrenalectomy as curative treatment, and the diagnosis of cystic lymphangioma of the left adrenal gland was confirmed at histology. The postoperative course was uneventful.ConclusionThis case report and review of the literature bring new insights into the diagnostic difficulty and management of cystic lymphangioma of the adrenal gland.

Adrenal Lymphangioma Clinically Mimicking a Cystic Pheochromocytoma: a Case Report and Literature Review

“…They are surrounded by a fibrous wall devoid of an epithelial lining [11]. The first case of adrenal cystic lymphangioma had been reported in 1965; recently, approximately 69 immunohistochemically cases have been reported in the literature [10][11][12][13]. Lymphangiomas are benign cystic vascular lesions, most frequently discovered in childhood.…”

Cystic Lymphangioma: A Rare Disease of the Adrenal Gland

“…The location can be diverse and commonly occur in the neck or axilla (2). This tumour is less common in adult and most frequently occur in children and very rarely involves the abdomen(3).…”

Adrenal cysts-a report of four cases including one with bilateral involvement

“…Adrenal cystic lesions are rare with an incidence of 0.06% in general population. [1,2]. Various types of cystic lesions of the adrenal gland have been described and have been classified into epithelial cysts, endothelial cysts, pseudocysts and parasitic cysts [1].…”

“…[1,2]. Various types of cystic lesions of the adrenal gland have been described and have been classified into epithelial cysts, endothelial cysts, pseudocysts and parasitic cysts [1]. Tumors of the adrenal gland, both benign and malignant can also show cystic change and have to be considered in the differential diagnosis of cystic lesions of the adrenal gland [2].…”

“…Tumors of the adrenal gland, both benign and malignant can also show cystic change and have to be considered in the differential diagnosis of cystic lesions of the adrenal gland [2]. Lymphangioendotheliomas though common at other sites, are unusual in the adrenal glands and bilateral involvement is extremely rare [1,3].…”